Anesthetic and perioperative management of a patient with Bernard-Soulier syndrome.

Abstract

We describe a patient with Bernard-Soulier syndrome who underwent emergency laparotomy for intraabdominal bleeding. Presentation of this recent case highlights some of the anesthetic and perioperative implications of the disease. Briefly, perioperative and anesthetic management of patients with Bernard-Soulier syndrome should include platelet transfusions and choice of appropriate anesthetic drugs and techniques. The potential benefit of desmopressin and corticosteroids should be considered. Thrombelastography, if available, is also useful.

• Authors: Georgia Kostopanagiotou, Ioanna Siafaka, Constantinos Sikiotis, Vassilios Smyrniotis
• Journal: Journal of clinical anesthesia (J Clin Anesth) Vol. 16 Issue 6 Pg. 458-60 (Sep 2004) ISSN: 0952-8180 [Print] United States
• PMID: 15567653 (Publication Type: Case Reports, Journal Article)

Topics

• Adult
• Anesthesia (methods)
• Bernard-Soulier Syndrome (complications)
• Corpus Luteum
• Female
• Hemoperitoneum (etiology, surgery)
• Humans
• Perioperative Care
• Platelet Transfusion