[Carney's syndrome: a case report].

Abstract

The peculiar aspects of the clinico-pathological picture and surgical treatment of Carney's syndrome, a rare morbid association of multiple non-epithelial neoplasms of the stomach, lung and chromaffin tissue, are focused on and discussed on the basis of the observation of a clinical case. The patient was a 22-year-old male with a multiple stromal tumour of the stomach, oesophageal leiomyoma, a left thoracic terato-chondroid neoplasm and gallbladder adenomyoma, surgically treated in two stages: laparotomy for gastric resection and cholecystectomy followed by left thoracotomy for resection of the intrathoracic neoplasm and excision of the oesophageal leiomyoma. The postoperative course was characterised by low morbidity and healing was monitored by means of thorough follow-up examinations. The case reported here is classed among the variants of Carney's classical triad. A knowledge of the pathological associations of these uncommon tumours and their natural history is of great importance for implementing appropriate diagnostic and therapeutic protocols.

• Authors: Enrico Maselli, Fernando Prete
• Journal: Chirurgia italiana (Chir Ital) 2004 Jul-Aug Vol. 56 Issue 4 Pg. 579-83 ISSN: 0009-4773 [Print] Italy
• Vernacular Title: Sindrome di Carney: un contributo casistico.
• PMID: 15453001 (Publication Type: Case Reports, Journal Article)

Topics

• Adenomyoma (surgery)
• Adult
• Cholecystectomy
• Chondroma (diagnostic imaging, surgery)
• Esophageal Neoplasms (diagnostic imaging, surgery)
• Follow-Up Studies
• Gallbladder Neoplasms (surgery)
• Humans
• Laparotomy
• Leiomyoma (diagnostic imaging, surgery)
• Lung Neoplasms (diagnostic imaging, surgery)
• Lymph Node Excision
• Male
• Neoplasms, Multiple Primary (surgery)
• Radiography, Thoracic
• Stomach Neoplasms (diagnostic imaging, surgery)
• Syndrome
• Time Factors
• Tomography, X-Ray Computed