Abstract | INTRODUCTION: METHODS: A 25-year-old female patient with GSDIa developed hepatic adenoma and kidney failure despite dietary therapy. The patient underwent an SLKT from a cadaveric donor. RESULTS: The operative time was 8 hours without hemotransfusion. Only a transitory lactic acidosis was observed. Laboratory results normalized on postoperative day 7. The patient was discharged on postoperative day 9. After 4 months, the patient is in good condition with well-functioning kidney and liver allografts. CONCLUSION: Patients with end-stage renal disease secondary to GSDIa should be considered for SLKT, especially when the disease is in an early stage.
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Authors | F Panaro, E Andorno, G Basile, N Morelli, G Bottino, I Fontana, M Bertocchi, S DiDomenico, M Miggino, L Saltalamacchia, D Ghinolfi, L Bonifazio, T M Jarzembowski, U Valente |
Journal | Transplantation proceedings
(Transplant Proc)
Vol. 36
Issue 5
Pg. 1483-4
(Jun 2004)
ISSN: 0041-1345 [Print] United States |
PMID | 15251364
(Publication Type: Case Reports, Journal Article)
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Copyright | Copyright 2004 Elsevier Inc. |
Topics |
- Adult
- Female
- Glycogen Storage Disease Type I
(pathology, surgery)
- Hepatectomy
- Humans
- Kidney Transplantation
- Liver
(pathology)
- Liver Transplantation
- Renal Dialysis
- Treatment Outcome
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