[Treatment of extreme obesity in a case of Prader-Willi-Labhart-syndrome (author's transl)].

Abstract

A boy 14 years of age, weighing 93,45 kg and 143 cm in height was refered to our clinic with hyperphagia and pain in the joints. The patient showed the Prader-Labhart-Willi-syndrome. Through maximal diet therapy, 2 admittances in our ward and through intensive psychological outpatient care, we have seen a weight loss of 26 kg in 18 months and clear improvement in the patient's health. We would like to draw attention to the fact that a weight reduction diet is a cooperative family effort. To satiate uncontrollable hunger an intermittent dose of Fenfluramine (0,5 mg/kg) is recommended.

• Authors: K Widhalm, J Deutsch
• Journal: Padiatrie und Padologie (Padiatr Padol) Vol. 11 Issue 1 Pg. 297-304 ( 1976) ISSN: 0030-9338 [Print] Austria
• Vernacular Title: Behandlung der exzessiven Adipositas am Beispiel des Prader-Willi-Labhart-Syndroms
• PMID: 1250628 (Publication Type: Case Reports, English Abstract, Journal Article)

Chemical References

• Fenfluramine

Topics

• Adolescent
• Carbohydrate Metabolism, Inborn Errors (diet therapy)
• Fenfluramine (therapeutic use)
• Humans
• Hyperplasia (diagnosis)
• Intellectual Disability (therapy)
• Male
• Metabolism, Inborn Errors
• Obesity (diagnosis, diet therapy)
• Psychotherapy