Abstract | STUDY OBJECTIVES: METHODS: We report a case of a 16-yr-old female with this syndrome. She underwent a laparoscopic bilateral gonadectomy and salpingectomy. A histopathological examination revealed gonadoblastoma with focal malignant dysgerminoma in the left dysgenetic gonad and an immunohistochemical of these fairly rare, malignant tumors. An androgen receptor was coded. Analysis was done. RESULTS: CONCLUSIONS:
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Authors | Minna M Joki-Erkkilä, Riitta Karikoski, Immo Rantala, Hanna-Liisa Lenko, Tapio Visakorpi, Pentti K Heinonen |
Journal | Journal of pediatric and adolescent gynecology
(J Pediatr Adolesc Gynecol)
Vol. 15
Issue 3
Pg. 145-9
(Jun 2002)
ISSN: 1083-3188 [Print] United States |
PMID | 12106750
(Publication Type: Case Reports, Journal Article)
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Chemical References |
- Receptors, Androgen
- Inhibins
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Topics |
- Adolescent
- Denys-Drash Syndrome
(diagnosis, metabolism, surgery)
- Dysgerminoma
(complications, diagnosis, metabolism, surgery)
- Female
- Gonadal Dysgenesis, 46,XY
(complications, diagnosis)
- Gonadoblastoma
(complications, diagnosis, metabolism, surgery)
- Gonads
(abnormalities, chemistry, surgery)
- Gynecologic Surgical Procedures
- Humans
- Immunohistochemistry
- Inhibins
(analysis)
- Kidney Failure, Chronic
(complications)
- Laparoscopy
- Ovarian Neoplasms
(complications, diagnosis, metabolism, surgery)
- Receptors, Androgen
(genetics)
- Treatment Outcome
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