[Dietary recommendations for pregnant women affected with phenylketonuria].

Abstract

Prevention of embryopathy due to maternal phenylketonuria is possible thanks to a maternal-specific low-phenylalanine diet, which has to be started before conception and followed during the whole gestation. The setup of this diet implies knowing the recommended dietary allowances for normal pregnant women as well as for women with nutritional deficiencies. Women with phenylketonuria must be considered at risk for nutritional imbalance for two main reasons. First, most adult women with phenylketonuria have been on a vegetarian diet for many years without protein substitutes or medical control. Secondly, the strict diet for pregnant women with phenylketonuria may induce anorexia or nutritional deficits if it is not well tolerated or understood. Protein, iron, calcium, selenium, vitamin B 12 and caloric intakes are the most sensitive parameters. Close cooperation with an experienced medical and dietician team is required.

• Authors: V Abadie, E Depondt, J L Bresson, M Vidailhet
• Journal: Archives de pediatrie : organe officiel de la Societe francaise de pediatrie (Arch Pediatr) Vol. 8 Issue 4 Pg. 397-406 (Apr 2001) ISSN: 0929-693X [Print] France
• Vernacular Title: Recommandations diététiques pour les femmes enceintes atteintes de phénylcétonurie.
• PMID: 11339133 (Publication Type: English Abstract, Journal Article)

Chemical References

• Phenylalanine

Topics

• Adult
• Diet
• Female
• Humans
• Nutrition Policy
• Nutritional Status
• Phenylalanine
• Phenylketonuria, Maternal (pathology, therapy)
• Pregnancy
• Risk Factors