Abstract |
We reviewed the clinical spectrum and possible prognostic factors in 14 children with restrictive cardiomyopathy. The patients were not homogeneous in clinical presentation or morphology. The mortality rate was high: 21.4% at 1 year and 50% at 2 years after presentation. Younger patients with respiratory symptoms, thromboembolism, increased cardiothoracic ratio on chest radiogram or patients with endocardial fibroelastosis appear to have a worse prognosis and orthotopic cardiac transplantation may be indicated.
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Authors | S C Chen, I C Balfour, S Jureidini |
Journal | The Journal of heart and lung transplantation : the official publication of the International Society for Heart Transplantation
(J Heart Lung Transplant)
Vol. 20
Issue 1
Pg. 90-2
(Jan 2001)
ISSN: 1053-2498 [Print] United States |
PMID | 11166616
(Publication Type: Comparative Study, Journal Article)
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Chemical References |
- Angiotensin-Converting Enzyme Inhibitors
- Diuretics
- Vasodilator Agents
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Topics |
- Adolescent
- Angiotensin-Converting Enzyme Inhibitors
(therapeutic use)
- Biopsy
- Cardiac Catheterization
- Cardiomyopathy, Restrictive
(diagnosis, mortality, physiopathology, therapy)
- Child
- Child, Preschool
- Diagnosis, Differential
- Disease Progression
- Diuretics
(therapeutic use)
- Drug Therapy, Combination
- Echocardiography, Doppler
- Electrocardiography
- Female
- Heart Transplantation
- Humans
- Infant
- Male
- Myocardial Contraction
- Prognosis
- Radiography, Thoracic
- Retrospective Studies
- Severity of Illness Index
- Survival Rate
- Vasodilator Agents
(therapeutic use)
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