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Ebstein's anomaly with coarctation of the aorta. An unusual association.

Abstract
Ebstein's anomaly with coarctation of the aorta is an extremely unusual condition. In this report, the clinical and surgical features of 3 male patients, aged 7 months, 4 years and 14 years, are discussed. All patients were in situs solitus. The first 2 patients had atrioventricular and ventriculoarterial discordance and progressed to heart failure in the neonatal period. The third had atrioventricular and ventriculoarterial concordance, as well as Wolf-Parkinson-White syndrome, with frequent episodes of paroxysmal tachycardia. The 3 patients underwent surgery for correction of the coarctation of the aorta. The patient with atrioventricular and ventriculoarterial concordance underwent tricuspid valvuloplasty using a DeVega-like technique. In addition, ablation of 2 anomalous pathways (Kent bundle), which were detected by the electrophysiologic study, was also subsequently performed. The 3 patients showed a good postoperative outcome for 2 years, although, in those with discordance, the surgical procedure did not influence the dysplasia of the tricuspid valve, because this valve showed light to moderate dysfunction.
AuthorsM Ebaid, E Azeka, N M Ikari, E A Sosa, M B Marcial, E Atik
JournalArquivos brasileiros de cardiologia (Arq Bras Cardiol) Vol. 73 Issue 2 Pg. 219-24 (Aug 1999) ISSN: 0066-782X [Print] Brazil
PMID10752191 (Publication Type: Case Reports, Journal Article)
Topics
  • Adolescent
  • Aortic Coarctation (complications, diagnosis, surgery)
  • Child, Preschool
  • Ebstein Anomaly (complications, diagnosis)
  • Electrocardiography
  • Heart Valve Diseases (diagnosis, surgery)
  • Humans
  • Infant
  • Male
  • Tricuspid Valve (surgery)

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