Incontinentia pigmenti: overcoming cosmetic challenges.

Abstract

Incontinentia pigmenti is a rare syndrome of genetic origin that affects the melanin production of the melanocytes in the epidermis or superficial dermis. It is an X-linked dominate disease with lethality in males. The syndrome presents with skin and dental manifestations similar to ectodermal dysplasia and congenital syphilis. However, dental alternatives for achieving esthetic reconstruction differ. This article illustrates a case of cosmetic rehabilitation of an 18-year-old woman with incontinentia pigmenti.

• Authors: J S Rouse
• Journal: Compendium of continuing education in dentistry (Jamesburg, N.J. : 1995) (Compend Contin Educ Dent) Vol. 20 Issue 11 Pg. 1034-6, 1038, 1040-1 (Nov 1999) ISSN: 1548-8578 [Print] United States
• PMID: 10650389 (Publication Type: Case Reports, Journal Article)

Chemical References

• Dental Porcelain

Topics

• Adolescent
• Dental Porcelain
• Dental Veneers
• Denture, Partial, Fixed
• Female
• Humans
• Incontinentia Pigmenti (complications, rehabilitation)
• Tooth Abnormalities (etiology, rehabilitation)