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XX Disorders of Sex Development 46 (Female Pseudohermaphroditism)

Congenital conditions in individuals with a female karyotype, in which the development of the gonadal or anatomical sex is atypical.
Also Known As:
Female Pseudohermaphroditism; Pseudohermaphroditism, Female; 46, XX Disorders of Sex Development; 46, XX DSD; 46,XX DSD; 46,XX Disorders of Sex Development; Female Pseudohermaphroditisms; Pseudohermaphroditisms, Female
Networked: 77 relevant articles (0 outcomes, 5 trials/studies)

Disease Context: Research Results

Related Diseases

1. Ovotesticular Disorders of Sex Development
2. Hyperplasia
3. Pituitary ACTH Hypersecretion
4. Lupus Nephritis
5. Leukemia

Experts

1. Fukami, Maki: 3 articles (01/2022 - 05/2009)
2. Koopman, Peter: 2 articles (01/2022 - 11/2016)
3. Sinclair, Andrew: 2 articles (01/2022 - 01/2016)
4. Khadilkar, Vaman: 2 articles (01/2021 - 11/2016)
5. Guaragna-Filho, Guilherme: 2 articles (01/2019 - 11/2012)
6. Hasegawa, Tomonobu: 2 articles (01/2019 - 05/2009)
7. Ogata, Tsutomu: 2 articles (01/2019 - 05/2009)
8. Eggers, Stefanie: 2 articles (11/2016 - 01/2016)
9. Horikawa, Reiko: 2 articles (05/2009 - 01/2004)
10. Bowles, Josephine: 1 article (01/2022)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to XX Disorders of Sex Development 46:
1. CortisoneFDA Link
2. EnzymesIBA
3. SteroidsIBA
4. Glucocorticoid Receptors (Glucocorticoid Receptor)IBA
5. Prednisone (Sone)FDA LinkGeneric
6. Protein Isoforms (Isoforms)IBA
7. Nitric Oxide Synthase (NO Synthase)IBA
8. AndrogensIBA
9. Steroid 21-Hydroxylase (21 Hydroxylase)IBA
10. Hormones (Hormone)IBA

Therapies and Procedures

1. Therapeutics
2. Female Circumcision (Infibulation)
3. Phalloplasty
4. Colostomy
5. Adrenalectomy