A rare, inherited platelet disorder characterized by a selective deficiency in the number and contents of platelet alpha-granules. It is associated with THROMBOCYTOPENIA, enlarged platelets, and prolonged bleeding time.
Also Known As:
Grey Platelet Syndrome; Platelet alpha-Granule Deficiency; Gray Platelet Syndromes; Grey Platelet Syndromes; Platelet Syndromes, Grey; Platelet alpha Granule Deficiency; Platelet alpha-Granule Deficiencies; Syndrome, Gray Platelet; Syndrome, Grey Platelet; Syndromes, Gray Platelet; alpha-Granule Deficiencies, Platelet; alpha-Granule Deficiency, Platelet