A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change.
Also Known As:
Usual Interstitial Pneumonia; Cryptogenic Fibrosing Alveolitides; Fibrosing Alveolitides, Cryptogenic; Fibrosing Alveolitis, Cryptogenic; Idiopathic Pulmonary Fibroses; Interstitial Pneumonia, Usual; Interstitial Pneumonias, Usual; Pulmonary Fibroses, Idiopathic; Pulmonary Fibrosis, Idiopathic; Usual Interstitial Pneumonias; Cryptogenic Fibrosing Alveolitis