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1-Pyrroline-5-Carboxylate Dehydrogenase (1 Pyrroline 5 Carboxylate Dehydrogenase)

An enzyme that catalyzes the oxidation of 1-pyrroline-5-carboxylate to L-GLUTAMATE in the presence of NAD. Defects in the enzyme are the cause of hyperprolinemia II.
Also Known As:
1 Pyrroline 5 Carboxylate Dehydrogenase; Delta(1)-Pyrroline-5-Carboxylate Dehydrogenase; GGS Dehydrogenase; Glutamic-Gamma-Semialdehyde Dehydrogenase; Glutamyl-Gamma-Semialdehyde Dehydrogenase; NADP+ Specific 8-Glutamate Semialdehyde Dehydrogenase; Dehydrogenase, 1-Pyrroline-5-Carboxylate; Dehydrogenase, GGS; Dehydrogenase, Glutamic-Gamma-Semialdehyde; Dehydrogenase, Glutamyl-Gamma-Semialdehyde; Glutamic Gamma Semialdehyde Dehydrogenase; Glutamyl Gamma Semialdehyde Dehydrogenase; NADP+ Specific 8 Glutamate Semialdehyde Dehydrogenase
Networked: 2 relevant articles (0 outcomes, 0 trials/studies)

Bio-Agent Context: Research Results

Experts

1. Garcia-Sanchez, Alfredo: 1 article (01/2007)
2. Hughes, Valerie: 1 article (01/2007)
3. Sales, Jill: 1 article (01/2007)
4. Smith, Stuart: 1 article (01/2007)
5. Stevenson, Karen: 1 article (01/2007)
6. Bavaresco, Caren Serra: 1 article (11/2003)
7. Chiarani, Fábria: 1 article (11/2003)
8. Delwing, Daniela: 1 article (11/2003)
9. Dutra-Filho, Carlos Severo: 1 article (11/2003)
10. Wajner, Moacir: 1 article (11/2003)

Related Diseases

1. Infections
2. Hyperprolinemia type 2

Related Drugs and Biologics

1. Endopeptidase Clp
2. Acyl-CoA Dehydrogenase (Medium-Chain Acyl-Coenzyme A Dehydrogenase)
3. Peptidylprolyl Isomerase (Prolyl Isomerase)
4. Thiosulfate Sulfurtransferase (Rhodanese)
5. Proteins (Proteins, Gene)
6. Proline (L-Proline)
7. Luciferases
8. Mixed Function Oxygenases (Monooxygenases)
9. Hydro-Lyases (Dehydratases)
10. Heat-Shock Proteins (Heat-Shock Protein)