Ovotesticular Disorders of Sex Development

Conditions of sexual ambiguity in which the individual possesses gonadal tissues of both sexes, tissues from the OVARY and the TESTIS. There can be a testis on one side and an ovary on the other (lateral), or there may be combined ovarian and testicular tissue (ovotestes) on each side (bilateral). The karyotype may be 46,XX; 46,XY; or a mosaic of 46,XX/46,XY. These disorders have historically been called true hermaphroditism.
Also Known As:
Familial True Hermaphroditism; Familial XX True Hermaphroditism; Ovotesticular DSD; True Hermaphroditism; DSD, Ovotesticular; DSDs, Ovotesticular; Familial True Hermaphroditisms; Hermaphroditism, Familial True; Hermaphroditisms, Familial True; Hermaphroditisms, True; Ovotesticular DSDs; True Hermaphroditism, Familial; True Hermaphroditisms; True Hermaphroditisms, Familial; Hermaphroditism, True
Networked: 56 relevant articles (0 outcomes, 7 trials/studies)

Disease Context: Research Results

Related Diseases

1. Gonadal Dysgenesis (Gonadal Agenesis)
2. Disorders of Sex Development (Intersexuality)
3. XX Disorders of Sex Development 46 (Female Pseudohermaphroditism)
4. Androgen-Insensitivity Syndrome (Testicular Feminization)
5. Mixed Gonadal Dysgenesis


1. de la Muela, Mercedes Sánchez: 1 article (07/2015)
2. Sathe, Pragati A: 1 article (07/2015)
3. Pérez-Gutiérrez, José F: 1 article (07/2015)
4. Sanghvi, Beejal V: 1 article (07/2015)
5. Bandgar, Tushar: 1 article (07/2015)
6. Sánchez-Calabuig, María J: 1 article (07/2015)
7. García-Pérez, Enrique: 1 article (07/2015)
8. Kasaliwal, Rajeev: 1 article (07/2015)
9. Budyal, Sweta R: 1 article (07/2015)
10. García-Botey, Concepción: 1 article (07/2015)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Ovotesticular Disorders of Sex Development:
1. H-Y AntigenIBA
2. Complement System Proteins (Complement)IBA
3. Testosterone (Sustanon)FDA Link
4. Androgen Receptors (Androgen Receptor)IBA
5. Protein Isoforms (Isoforms)IBA
6. Nitric Oxide Synthase (NO Synthase)IBA
7. Mosaic variegated aneuploidy syndromeIBA
8. N 30IBA
9. XXY syndromeIBA
10. OxidoreductasesIBA

Therapies and Procedures

1. Laparotomy
2. Orchiopexy
3. Transplantation (Transplant Recipients)
4. Ovariectomy (Oophorectomy)
5. Orchiectomy (Orchidectomy)