An autosomal dominant disorder characterized by degeneration of the THALAMUS and progressive insomnia. It is caused by a mutation in the prion protein (PRIONS).
Also Known As:
Insomnia, Fatal Familial; Familial Fatal Insomnia; Insomnia Familial Fatal; Familial Fatal Insomnias; Familial Fatal, Insomnia; Familial Fatals, Insomnia; Fatal Familial Insomnias; Fatal Insomnia, Familial; Fatal Insomnias, Familial; Fatal, Insomnia Familial; Fatals, Insomnia Familial; Insomnia Familial Fatals; Insomnia, Familial Fatal; Insomnias, Familial Fatal; Insomnias, Fatal Familial