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Hypokalemic Periodic Paralysis (Periodic Paralysis, Hypokalemic)

An autosomal dominant familial disorder characterized by recurrent episodes of skeletal muscle weakness associated with falls in serum potassium levels. The condition usually presents in the first or second decade of life with attacks of trunk and leg paresis during sleep or shortly after awakening. Symptoms may persist for hours to days and generally are precipitated by exercise or a meal high in carbohydrates. (Adams et al., Principles of Neurology, 6th ed, p1483)
Also Known As:
Periodic Paralysis, Hypokalemic; HOKPP; HYPOKPP; HYPOPP; Hypokalemic Periodic Paralysis, Familial; Periodic Paralysis- Hypokalemic; Westphall Disease; Periodic Paralysis Hypokalemic; Periodic Paralysis- Hypokalemics; Familial Hypokalemic Periodic Paralysis; Paralysis, Hypokalemic Periodic; Primary Hypokalemic Periodic Paralysis
Networked: 357 relevant articles (14 outcomes, 19 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Paralysis (Palsy)
2. Hypokalemic Periodic Paralysis (Periodic Paralysis, Hypokalemic)
3. Myotonia
4. Channelopathies
5. Thyrotoxicosis

Experts

1. Cannon, Stephen C: 11 articles (01/2022 - 07/2007)
2. Jurkat-Rott, Karin: 11 articles (07/2019 - 04/2002)
3. Lehmann-Horn, Frank: 10 articles (07/2019 - 04/2002)
4. Fontaine, Bertrand: 7 articles (11/2018 - 01/2008)
5. Lin, Shih-Hua: 7 articles (05/2014 - 01/2003)
6. Sternberg, Damien: 6 articles (11/2018 - 05/2007)
7. Wu, Fenfen: 5 articles (11/2021 - 10/2011)
8. Hanna, Michael G: 5 articles (11/2019 - 10/2010)
9. Kim, June-Bum: 5 articles (10/2014 - 01/2010)
10. Meola, G: 5 articles (05/2009 - 10/2005)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Hypokalemic Periodic Paralysis:
1. PotassiumIBA
2. Acetazolamide (Diamox)FDA LinkGeneric
3. Dichlorphenamide (Daranide)FDA Link
4. Potassium Channels (Potassium Channel)IBA
5. Arginine (L-Arginine)FDA Link
6. Carbonic Anhydrase InhibitorsIBA
7. Pinacidil (Pindac)FDA Link
8. Mexiletine (Mexitil)FDA LinkGeneric
9. Sodium Channels (Sodium Channel)IBA
10. CarbohydratesIBA

Therapies and Procedures

1. Therapeutics
2. Thymectomy
3. Intravenous Infusions
4. Electrodes (Electrode)
5. Epidural Analgesia