Inflammation of blood vessels within the central nervous system. Primary vasculitis is usually caused by autoimmune or idiopathic factors, while secondary vasculitis is caused by existing disease process. Clinical manifestations are highly variable but include HEADACHE; SEIZURES; behavioral alterations; INTRACRANIAL HEMORRHAGES; TRANSIENT ISCHEMIC ATTACK; and BRAIN INFARCTION. (From Adams et al., Principles of Neurology, 6th ed, pp856-61)
Also Known As:
Vasculitis, Central Nervous System; CNS Vasculitis; Central Nervous System Angiitis; Granulomatous Arteritis; Primary Central Nervous System Vasculitis; Vasculitis, CNS, Secondary; Angiitis, Cerebral; Angiitis, Granulomatous; Arteritis, Granulomatous; Arteritis, Postzoster; CNS Vasculitis, Primary; CNS Vasculitis, Secondary; Vasculitis, CNS; Vasculitis, Cerebral; Vasculitis, Primary CNS; Vasculitis, Secondary CNS; Angiitis, Central Nervous System; Cerebral Angiitis; Cerebral Vasculitis; Granulomatous Angiitis; Postzoster Arteritis; Primary CNS Vasculitis; Secondary CNS Vasculitis