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alpha 1-Antitrypsin Deficiency (alpha 1 Antitrypsin Deficiency)

Deficiency of the protease inhibitor ALPHA 1-ANTITRYPSIN that manifests primarily as PULMONARY EMPHYSEMA and LIVER CIRRHOSIS.
Also Known As:
alpha 1 Antitrypsin Deficiency; Deficiencies, alpha 1-Antitrypsin; Deficiency, alpha 1-Antitrypsin; alpha 1-Antitrypsin Deficiencies
Networked: 216 relevant articles (6 outcomes, 14 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Liver Diseases (Liver Disease)
2. Panniculitis
3. Hepatolenticular Degeneration (Wilson's Disease)
4. Hepatitis B
5. Emphysema

Experts

1. Krowka, Michael J: 2 articles (08/2013 - 02/2011)
2. Stockley, Robert A: 2 articles (01/2010 - 06/2006)
3. Stockley, R A: 2 articles (08/2003 - 01/2001)
4. Feijó, Salvato: 1 article (11/2014)
5. Silva, Sónia: 1 article (11/2014)
6. Amaral, Cecília Beatriz Alves: 1 article (11/2014)
7. Laverdure, Noémie: 1 article (10/2014)
8. Alex-Cordier, Marie Pierre: 1 article (10/2014)
9. Lachaux, Alain: 1 article (10/2014)
10. Dabadie, Alain: 1 article (10/2014)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to alpha 1-Antitrypsin Deficiency:
1. alpha 1-Antitrypsin (alpha 1 Antitrypsin)IBA
2. Leukocyte Elastase (Neutrophil Elastase)IBA
3. alpha-Macroglobulins (alpha 2 Macroglobulin)IBA
4. DNA (Deoxyribonucleic Acid)IBA
5. CopperIBA
6. Hepatitis B AntigensIBA
7. Protease Inhibitors (Protease Inhibitor)IBA
8. Carbon MonoxideIBA
9. AntigensIBA
10. Primary sclerosing cholangitisIBA

Therapies and Procedures

1. Liver Transplantation
2. Transplants (Transplant)
3. Lung Transplantation
4. Transplantation (Transplant Recipients)
5. Heart-Lung Transplantation