A congenital heart defect characterized by the narrowing or complete absence of the opening between the RIGHT VENTRICLE and the PULMONARY ARTERY. Lacking a normal PULMONARY VALVE, unoxygenated blood in the right ventricle can not be effectively pumped into the lung for oxygenation. Clinical features include rapid breathing, CYANOSIS, right ventricle atrophy, and abnormal heart sounds (HEART MURMURS).
Also Known As:
Pulmonary Valve Atresia; Atresia, Pulmonary Valve; Atresias, Pulmonary; Atresias, Pulmonary Valve; Pulmonary Atresias; Pulmonary Valve Atresias; Valve Atresia, Pulmonary; Valve Atresias, Pulmonary; Atresia, Pulmonary