An interstitial lung disease of unknown etiology, occurring between 21-80 years of age. It is characterized by a dramatic onset of a "pneumonia-like" illness with cough, fever, malaise, fatigue, and weight loss. Pathological features include prominent interstitial inflammation without collagen fibrosis, diffuse fibroblastic foci, and no microscopic honeycomb change. There is excessive proliferation of granulation tissue within small airways and alveolar ducts.
Also Known As:
Cryptogenic Organizing Pneumonias; Organizing Pneumonia, Cryptogenic; Organizing Pneumonia, Primary; Organizing Pneumonias, Primary; Pneumonia, Cryptogenic Organizing; Pneumonia, Primary Organizing; Primary Organizing Pneumonias; BOOP Bronchiolitis Obliterans Organizing Pneumonia; Bronchiolitis Obliterans Organizing Pneumonia; Primary Organizing Pneumonia