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Aggressive Fibromatosis (Desmoid)

A childhood counterpart of abdominal or extra-abdominal desmoid tumors, characterized by firm subcutaneous nodules that grow rapidly in any part of the body but do not metastasize. The adult form of abdominal fibromatosis is FIBROMATOSIS, ABDOMINAL. (Stedman, 25th ed)
Also Known As:
Desmoid; Fibromatosis, Aggressive; Aggressive Fibromatoses; Desmoids; Fibromatoses, Aggressive
Networked: 1254 relevant articles (99 outcomes, 151 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Neoplasms (Cancer)
2. Fibroma (Fibromatosis)
3. Aggressive Fibromatosis (Desmoid)
4. Sarcoma (Soft Tissue Sarcoma)
5. Adenomatous Polyposis Coli (Familial Adenomatous Polyposis)

Experts

1. Nishida, Yoshihiro: 27 articles (01/2022 - 07/2009)
2. Alman, Benjamin A: 15 articles (01/2022 - 05/2002)
3. Hamada, Shunsuke: 14 articles (01/2022 - 01/2014)
4. Lazar, Alexander J: 11 articles (01/2022 - 08/2011)
5. Sakai, Tomohisa: 11 articles (01/2022 - 02/2016)
6. Ishiguro, Naoki: 11 articles (12/2019 - 07/2009)
7. Colombo, Chiara: 10 articles (01/2021 - 08/2011)
8. Bonvalot, Sylvie: 9 articles (01/2022 - 06/2003)
9. Ikuta, Kunihiro: 9 articles (01/2022 - 01/2014)
10. Koike, Hiroshi: 9 articles (01/2022 - 08/2017)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Aggressive Fibromatosis:
1. TamoxifenFDA LinkGeneric
2. Methotrexate (Mexate)FDA LinkGeneric
3. Meloxicam (Mobic)FDA LinkGeneric
4. Sulindac (Copal)FDA LinkGeneric
5. Doxorubicin (Adriamycin)FDA LinkGeneric
6. Imatinib Mesylate (Gleevec)FDA Link
7. Vinblastine (Vinblastine Sulfate)FDA Link
8. nirogacestatIBA
9. CateninsIBA
10. Sorafenib (BAY 43-9006)FDA Link

Therapies and Procedures

1. Radiotherapy
2. Drug Therapy (Chemotherapy)
3. Therapeutics
4. Colectomy
5. Cryosurgery