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Desmoplastic Fibroma

An extremely rare bone tumor characterized by abundant collagen formation and a fibrous stroma, without evidence of mitosis or pleomorphism. It appears on x-rays as an osteolytic lesion with well-defined margins and must be differentiated from primary fibrosarcoma of bone. (DeVita Jr et al., Cancer: Principles & Practice of Oncology, 3d ed, p1441)
Also Known As:
Fibroma, Desmoplastic; Collagenous Fibroma; Desmoplastic Fibroblastoma; Collagenous Fibromas; Desmoplastic Fibroblastomas; Desmoplastic Fibromas; Fibroblastoma, Desmoplastic; Fibroma, Collagenous
Networked: 42 relevant articles (1 outcomes, 3 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Aggressive Fibromatosis (Desmoid)
2. Neoplasms (Cancer)
3. Fibroma (Fibromatosis)
4. Osteofibrous Dysplasia
5. Sarcoma (Soft Tissue Sarcoma)

Experts

1. Kaneko, Kazuo: 2 articles (05/2014 - 01/2013)
2. Okubo, Taketo: 2 articles (05/2014 - 01/2013)
3. Saito, Tsuyoshi: 2 articles (05/2014 - 01/2013)
4. Suehara, Yoshiyuki: 2 articles (05/2014 - 01/2013)
5. Takagi, Tatsuya: 2 articles (05/2014 - 01/2013)
6. Beatón-Comulada, David: 1 article (08/2022)
7. Bibiloni-Lugo, José P: 1 article (08/2022)
8. Bibiloni-Rodríguez, Juan: 1 article (08/2022)
9. Colón-Miranda, Roberto: 1 article (08/2022)
10. Ramírez, Norman: 1 article (08/2022)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Desmoplastic Fibroma:
1. beta CateninIBA
2. Cyclin D1IBA
3. ParaffinIBA
4. NestinIBA
5. CollagenIBA
6. VimentinIBA
7. CateninsIBA
8. RNA (Ribonucleic Acid)IBA
9. Claudin-1IBA
10. Apolipoproteins D (Apo D)IBA

Therapies and Procedures

1. Therapeutics
2. Curettage
3. Bone Transplantation (Bone Grafting)
4. Operative Surgical Procedures
5. Spinal Fusion (Spondylosyndesis)