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CREST Syndrome (Syndrome, CREST)

A mild form of LIMITED SCLERODERMA, a multi-system disorder. Its features include symptoms of CALCINOSIS; RAYNAUD DISEASE; ESOPHAGEAL MOTILITY DISORDERS; sclerodactyly, and TELANGIECTASIS. When the defect in esophageal function is not prominent, it is known as CRST syndrome.
Also Known As:
Syndrome, CREST; Calcinosis, Raynaud's phenomenon, Esophageal dismobility, Sclerodactyly, Telangiectasia Syndrome; Calcinosis-Raynaud Phenomenon-Sclerodactyly-Telangiectasia; CREST Syndromes; CRST Syndromes; Calcinosis Raynaud Phenomenon Sclerodactyly Telangiectasia; Phenomenon-Sclerodactyly-Telangiectasia, Calcinosis-Raynaud; Syndrome, CRST; CRST Syndrome
Networked: 185 relevant articles (2 outcomes, 14 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Telangiectasis (Telangiectasia)
2. Calcinosis
3. Biliary Liver Cirrhosis (Primary Biliary Cirrhosis)
4. Systemic Scleroderma (Systemic Sclerosis)
5. Systemic Lupus Erythematosus (Libman-Sacks Disease)

Experts

1. Ikeda, S: 2 articles (07/2001 - 05/2001)
2. Ber, Charles-Eric: 1 article (12/2022)
3. Dumortier, Jérôme: 1 article (12/2022)
4. Lambin, Thomas: 1 article (12/2022)
5. Lupu, Alexandru: 1 article (12/2022)
6. Pioche, Mathieu: 1 article (12/2022)
7. Rivory, Jérôme: 1 article (12/2022)
8. Valette, Pierre-Jean: 1 article (12/2022)
9. Balan, Gabriela: 1 article (01/2022)
10. Bobeica, Carmen: 1 article (01/2022)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to CREST Syndrome:
1. Norethindrone (Norethisterone)FDA LinkGeneric
2. Ethinyl Estradiol (Estinyl)FDA LinkGeneric
3. AntibodiesIBA
4. Antinuclear AntibodiesIBA
5. CalciumIBA
6. anticentromere antibodyIBA
7. ChromatinIBA
8. Captopril (Capoten)FDA LinkGeneric
9. anti-scl-70 autoantibodiesIBA
10. GhrelinIBA

Therapies and Procedures

1. Gas Lasers
2. Therapeutics
3. Argon Plasma Coagulation
4. Catheters
5. Dye Lasers