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Epidermolysis Bullosa Acquisita (Acquired Epidermolysis Bullosa)

Form of epidermolysis bullosa characterized by trauma-induced, subepidermal blistering with no family history of the disease. Direct immunofluorescence shows IMMUNOGLOBULIN G deposited at the dermo-epidermal junction.
Also Known As:
Acquired Epidermolysis Bullosa; Acquired Form of Epidermolysis Bullosa; Epidermolysis Bullosa, Acquired
Networked: 545 relevant articles (22 outcomes, 41 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Bullous Pemphigoid (Pemphigoid)
2. Lichen Planus (Lichen Ruber Planus)
3. Psoriasis (Pustulosis Palmaris et Plantaris)
4. Atopic Dermatitis (Atopic Eczema)
5. Pyoderma Gangrenosum

Experts

1. Zillikens, Detlef: 73 articles (01/2022 - 06/2002)
2. Ludwig, Ralf J: 53 articles (10/2022 - 01/2011)
3. Schmidt, Enno: 38 articles (10/2022 - 06/2002)
4. Bieber, Katja: 28 articles (10/2022 - 01/2011)
5. Hashimoto, Takashi: 25 articles (03/2021 - 07/2002)
6. Kalies, Kathrin: 18 articles (12/2020 - 11/2011)
7. Sitaru, Cassian: 17 articles (10/2017 - 06/2002)
8. Kasperkiewicz, Michael: 15 articles (01/2022 - 01/2011)
9. Ishii, Norito: 14 articles (10/2020 - 01/2006)
10. Chen, Mei: 13 articles (02/2012 - 05/2002)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Epidermolysis Bullosa Acquisita:
1. Intravenous Immunoglobulins (IVIG)FDA Link
2. Cyclosporine (Ciclosporin)FDA LinkGeneric
3. Collagen Type VIIIBA
4. AutoantibodiesIBA
5. AntibodiesIBA
6. SaltsIBA
7. Matrix Metalloproteinases (MMPs)IBA
8. ColchicineFDA LinkGeneric
9. Monoclonal AntibodiesIBA
10. Adrenal Cortex Hormones (Corticosteroids)IBA

Therapies and Procedures

1. Therapeutics
2. Photopheresis
3. Lasers (Laser)
4. Organ Transplantation
5. Tracheostomy