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Churg-Strauss Syndrome (Allergic Angiitis)

Widespread necrotizing angiitis with granulomas. Pulmonary involvement is frequent. Asthma or other respiratory infection may precede evidence of vasculitis. Eosinophilia and lung involvement differentiate this disease from POLYARTERITIS NODOSA.
Also Known As:
Allergic Angiitis; Syndrome, Churg-Strauss; Vasculitis, Churg Strauss; Allergic Angiitis and Granulomatosis; Allergic Granulomatosis; Allergic Granulomatous and Angiitis; Eosinophilic Granulomatous Vasculitis; Granulomatous Allergic Angiitis; Allergic Angiitides; Allergic Angiitides, Granulomatous; Allergic Angiitis, Granulomatous; Allergic Granulomatoses; Allergic Granulomatous Angiitides; Angiitides, Allergic; Angiitides, Allergic Granulomatous; Angiitides, Granulomatous Allergic; Angiitis, Allergic; Angiitis, Granulomatous Allergic; Churg Strauss Syndrome; Churg-Strauss Vasculitis; Disorder, EGPA; Disorders, EGPA; EGPA Disorders; Granulomatoses, Allergic; Granulomatosis, Allergic; Granulomatous Allergic Angiitides; Granulomatous Angiitides, Allergic; Granulomatous Angiitis, Allergic; Granulomatous Vasculitides, Eosinophilic; Granulomatous Vasculitis, Eosinophilic; Vasculitides, Eosinophilic Granulomatous; Vasculitis, Eosinophilic Granulomatous; Allergic Granulomatous Angiitis; Angiitis, Allergic Granulomatous; EGPA Disorder; Eosinophilic Granulomatosis with Polyangiitis; Vasculitis, Churg-Strauss
Networked: 1196 relevant articles (85 outcomes, 54 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Microscopic Polyangiitis
2. Asthma (Bronchial Asthma)
3. Granulomatosis with Polyangiitis (Wegener's Granulomatosis)
4. Polyarteritis Nodosa (Periarteritis Nodosa)
5. Vasculitis (Vasculitides)

Experts

1. Guillevin, Loïc: 34 articles (01/2021 - 04/2003)
2. Pagnoux, Christian: 28 articles (05/2022 - 04/2003)
3. Specks, Ulrich: 20 articles (05/2022 - 09/2003)
4. Moosig, Frank: 18 articles (01/2022 - 06/2008)
5. Puéchal, Xavier: 18 articles (01/2021 - 10/2007)
6. Mouthon, Luc: 17 articles (01/2021 - 11/2003)
7. Wechsler, Michael E: 16 articles (10/2022 - 01/2002)
8. Gross, Wolfgang L: 16 articles (01/2014 - 05/2002)
9. Merkel, Peter A: 15 articles (05/2022 - 04/2003)
10. Vaglio, Augusto: 13 articles (05/2022 - 09/2007)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Churg-Strauss Syndrome:
1. mepolizumabIBA
2. Adrenal Cortex Hormones (Corticosteroids)IBA
3. Cyclophosphamide (Cytoxan)FDA LinkGeneric
4. Intravenous Immunoglobulins (IVIG)FDA Link
5. GlucocorticoidsIBA
6. benralizumabIBA
7. Rituximab (Mabthera)FDA Link
8. Interleukin-5 (Interleukin 5)IBA
9. Antineutrophil Cytoplasmic Antibodies (ANCA)IBA
10. Interferon-alpha (Interferon Alfa)IBA

Therapies and Procedures

1. Therapeutics
2. Remission Induction
3. Plasmapheresis
4. Plasma Exchange
5. Aftercare (After-Treatment)