Chronic inflammatory disease of the BILIARY TRACT. It is characterized by fibrosis and hardening of the intrahepatic and extrahepatic biliary ductal systems leading to bile duct strictures, CHOLESTASIS, and eventual BILIARY CIRRHOSIS.
Also Known As:
Cholangitis, Sclerosing; Cholangiitis, Sclerosing; Cholangitis, Primary Sclerosing; Primary Sclerosing Cholangitis; Cholangiitides, Sclerosing; Cholangitides, Primary Sclerosing; Cholangitides, Sclerosing; Primary Sclerosing Cholangitides; Sclerosing Cholangiitides; Sclerosing Cholangiitis; Sclerosing Cholangitides; Sclerosing Cholangitides, Primary; Sclerosing Cholangitis, Primary