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Uveomeningoencephalitic Syndrome (Vogt Koyanagi Harada Syndrome)

A syndrome characterized by bilateral granulomatous UVEITIS with IRITIS and secondary GLAUCOMA, premature ALOPECIA, symmetrical VITILIGO, poliosis circumscripta (a strand of depigmented hair), HEARING DISORDERS, and meningeal signs (neck stiffness and headache). Examination of the cerebrospinal fluid reveals a pattern consistent with MENINGITIS, ASEPTIC. (Adams et al., Principles of Neurology, 6th ed, p748; Surv Ophthalmol 1995 Jan;39(4):265-292)
Also Known As:
Vogt Koyanagi Harada Syndrome; Syndrome, VKH (Vogt Koyanagi Harada); Syndrome, Vogt Koyanagi Harada; VKH (Vogt Koyanagi Harada) Syndrome; VKH Syndrome; Vogt-Koyanagi-Harada Disease; Disease, Vogt-Koyanagi-Harada; Syndrome, Uveomeningoencephalitic; Syndrome, VKH; Syndrome, Vogt-Koyanagi-Harada; Uveomeningoencephalitides; VKH Syndrome (Vogt Koyanagi Harada); Vogt Koyanagi Harada Disease; Uveomeningoencephalitis; Vogt-Koyanagi-Harada Syndrome
Networked: 523 relevant articles (29 outcomes, 38 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Retinal Detachment (Retinal Detachments)
2. Uveitis
3. Sympathetic Ophthalmia (Sympathetic Uveitis)
4. Disease Progression
5. Panuveitis

Experts

1. Yang, Peizeng: 49 articles (01/2021 - 04/2002)
2. Kijlstra, Aize: 41 articles (01/2021 - 05/2007)
3. Hou, Shengping: 26 articles (11/2019 - 01/2008)
4. Namba, Kenichi: 12 articles (06/2022 - 12/2006)
5. Abu El-Asrar, Ahmed M: 11 articles (09/2022 - 10/2010)
6. Herbort, Carl P: 11 articles (06/2022 - 04/2007)
7. Du, Liping: 11 articles (11/2019 - 01/2008)
8. Qi, Jian: 10 articles (11/2019 - 12/2013)
9. Zhou, Yan: 10 articles (03/2015 - 08/2012)
10. Goto, Hiroshi: 9 articles (06/2022 - 07/2006)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Uveomeningoencephalitic Syndrome:
1. Adrenal Cortex Hormones (Corticosteroids)IBA
2. SteroidsIBA
3. Adalimumab (Humira)FDA Link
4. Triamcinolone Acetonide (Azmacort)FDA LinkGeneric
5. Immunosuppressive Agents (Immunosuppressants)IBA
6. Rituximab (Mabthera)FDA Link
7. Cyclosporine (Ciclosporin)FDA LinkGeneric
8. Dexamethasone (Maxidex)FDA LinkGeneric
9. Fluorescein (Funduscein)FDA LinkGeneric
10. GlucocorticoidsIBA

Therapies and Procedures

1. Therapeutics
2. Immunomodulation
3. Cochlear Implantation
4. Phacoemulsification
5. Drug Therapy (Chemotherapy)