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Persistent Truncus Arteriosus

A congenital anomaly caused by the failed development of TRUNCUS ARTERIOSUS into separate AORTA and PULMONARY ARTERY. It is characterized by a single arterial trunk that forms the outlet for both HEART VENTRICLES and gives rise to the systemic, pulmonary, and coronary arteries. It is always accompanied by a ventricular septal defect.
Also Known As:
Truncus Arteriosus, Persistent; Arteriosus Communis, Truncus; Truncus Arteriosus Communi; Truncus Arteriosus Communis
Networked: 40 relevant articles (0 outcomes, 2 trials/studies)

Disease Context: Research Results

Related Diseases

1. Ventricular Heart Septal Defects (Ventricular Septal Defect)
2. Tetralogy of Fallot (Fallot Tetralogy)
3. Pulmonary Atresia (Pulmonary Valve Atresia)
4. Double Outlet Right Ventricle
5. Pulmonary Valve Stenosis (Pulmonary Stenosis)

Experts

1. Dyer, Laura A: 2 articles (07/2021 - 06/2009)
2. Epstein, Jonathan A: 2 articles (02/2015 - 11/2006)
3. Lo, Cecilia W: 2 articles (02/2015 - 12/2004)
4. Yu, Qing: 2 articles (02/2015 - 12/2004)
5. Kirby, Margaret L: 2 articles (06/2009 - 12/2004)
6. Rugonyi, Sandra: 1 article (07/2021)
7. Guarque-Rus, Albert: 1 article (11/2020)
8. Landeyro, Julieta: 1 article (11/2020)
9. Martín-González, Lourdes: 1 article (11/2020)
10. Puerto-Tamayo, Linda Grace: 1 article (11/2020)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Persistent Truncus Arteriosus:
1. beta-cyclodextrin tetradecasulfate (CTDS)IBA
2. NimustineIBA
3. Semaphorins (Semaphorin)IBA
4. CalciumIBA
5. Caspase 3 (Caspase-3)IBA
6. Transcription Factor CHOPIBA
7. GATA6 Transcription FactorIBA
8. Vascular Endothelial Growth Factor A (Vascular Endothelial Growth Factor)IBA
9. Neuropilin-1IBA
10. Connexin 43 (Connexin43)IBA

Therapies and Procedures

1. Parasympathectomy
2. Extracorporeal Membrane Oxygenation
3. Replantation
4. Cardiopulmonary Bypass (Heart-Lung Bypass)
5. Anesthesia