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Pulmonary Veno-Occlusive Disease (Veno Occlusive Disease, Pulmonary)

Pathological process resulting in the fibrous obstruction of the small- and medium-sized PULMONARY VEINS and PULMONARY HYPERTENSION. Veno-occlusion can arise from fibrous proliferation of the VASCULAR INTIMA and VASCULAR MEDIA; THROMBOSIS; or a combination of both.
Also Known As:
Veno Occlusive Disease, Pulmonary; Pulmonary Veno Occlusive Disease; Pulmonary Venoocclusive Disease; Diseases, Pulmonary Veno-Occlusive; Pulmonary Veno-Occlusive Diseases; Pulmonary Venoocclusive Diseases; Veno-Occlusive Diseases, Pulmonary; Venoocclusive Disease, Pulmonary; Venoocclusive Diseases, Pulmonary; Veno-Occlusive Disease, Pulmonary
Networked: 165 relevant articles (3 outcomes, 4 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Congenital Heart Defects (Congenital Heart Defect)
2. Connective Tissue Diseases (Connective Tissue Disease)
3. Portal Hypertension
4. Familial Primary Pulmonary Hypertension
5. Rare Diseases (Rare Disease)

Experts

1. Humbert, Marc: 15 articles (01/2021 - 03/2002)
2. Montani, David: 14 articles (01/2021 - 10/2009)
3. Sitbon, Olivier: 8 articles (01/2021 - 03/2002)
4. Dorfmüller, Peter: 8 articles (10/2020 - 09/2015)
5. Girerd, Barbara: 7 articles (01/2021 - 09/2015)
6. Savale, Laurent: 7 articles (01/2021 - 08/2010)
7. Perros, Frédéric: 6 articles (01/2021 - 09/2015)
8. Simonneau, Gérald: 6 articles (01/2019 - 07/2004)
9. Chaumais, Marie-Camille: 5 articles (01/2021 - 09/2015)
10. Jaïs, Xavier: 5 articles (01/2021 - 08/2010)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Pulmonary Veno-Occlusive Disease:
1. Epoprostenol (Prostacyclin)FDA LinkGeneric
2. Sorafenib (BAY 43-9006)FDA Link
3. 7-(N-(3-aminopropyl)amino)heptan-2-oneIBA
4. DNA (Deoxyribonucleic Acid)IBA
5. Mitomycin (Mitomycin-C)FDA LinkGeneric
6. Vasodilator Agents (Vasodilators)IBA
7. Phosphotransferases (Kinase)IBA
8. Prokaryotic Initiation Factor-2IBA
9. Imatinib Mesylate (Gleevec)FDA Link
10. Nitric Oxide (Nitrogen Monoxide)FDA Link

Therapies and Procedures

1. Therapeutics
2. Sutureless Surgical Procedures
3. Lung Transplantation
4. Drug Therapy (Chemotherapy)
5. Bone Marrow Transplantation (Transplantation, Bone Marrow)