A myeloproliferative disorder of unknown etiology, characterized by abnormal proliferation of all hematopoietic bone marrow elements and an absolute increase in red cell mass and total blood volume, associated frequently with splenomegaly, leukocytosis, and thrombocythemia. Hematopoiesis is also reactive in extramedullary sites (liver and spleen). In time myelofibrosis occurs.
Also Known As:
Polycythemia Ruba Vera; Primary Polycythemia; Disease, Osler-Vaquez; Erythremias; Osler Vaquez Disease; Polycythemia Ruba Veras; Polycythemia Rubra Veras; Polycythemia, Primary; Polycythemias, Primary; Primary Polycythemias; Ruba Vera, Polycythemia; Ruba Veras, Polycythemia; Vera, Polycythemia Ruba; Vera, Polycythemia Rubra; Veras, Polycythemia Ruba; Veras, Polycythemia Rubra; Erythremia; Osler-Vaquez Disease; Polycythemia Rubra Vera