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Polycythemia Vera

A myeloproliferative disorder of unknown etiology, characterized by abnormal proliferation of all hematopoietic bone marrow elements and an absolute increase in red cell mass and total blood volume, associated frequently with splenomegaly, leukocytosis, and thrombocythemia. Hematopoiesis is also reactive in extramedullary sites (liver and spleen). In time myelofibrosis occurs.
Also Known As:
Polycythemia Ruba Vera; Primary Polycythemia; Disease, Osler-Vaquez; Erythremias; Osler Vaquez Disease; Polycythemia Ruba Veras; Polycythemia Rubra Veras; Polycythemia, Primary; Polycythemias, Primary; Primary Polycythemias; Ruba Vera, Polycythemia; Ruba Veras, Polycythemia; Vera, Polycythemia Ruba; Vera, Polycythemia Rubra; Veras, Polycythemia Ruba; Veras, Polycythemia Rubra; Erythremia; Osler-Vaquez Disease; Polycythemia Rubra Vera
Networked: 2018 relevant articles (85 outcomes, 205 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Essential Thrombocythemia
2. Primary Myelofibrosis (Myelosclerosis)
3. Thrombocytosis (Thrombocythemia)
4. Thrombosis (Thrombus)
5. Neoplasms (Cancer)

Experts

1. Verstovsek, Srdan: 57 articles (01/2022 - 06/2006)
2. Vannucchi, Alessandro M: 52 articles (12/2022 - 09/2005)
3. Barbui, Tiziano: 48 articles (12/2022 - 01/2003)
4. Tefferi, Ayalew: 44 articles (10/2018 - 04/2002)
5. Hoffman, Ronald: 32 articles (12/2022 - 08/2007)
6. Finazzi, Guido: 32 articles (12/2019 - 01/2003)
7. Kiladjian, Jean-Jacques: 31 articles (12/2022 - 01/2003)
8. Prchal, Josef T: 28 articles (12/2022 - 06/2004)
9. Mascarenhas, John: 27 articles (12/2022 - 05/2009)
10. Guglielmelli, Paola: 27 articles (01/2021 - 09/2005)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Polycythemia Vera:
1. Hydroxyurea (Hydrea)FDA LinkGeneric
2. Aspirin (Acetylsalicylic Acid)FDA LinkGeneric
3. ruxolitinibIBA
4. InterferonsIBA
5. Interferon-alpha (Interferon Alfa)IBA
6. ErythropoietinFDA Link
7. Busulfan (Busulfex)FDA Link
8. Janus Kinase InhibitorsIBA
9. givinostatIBA
10. Imatinib Mesylate (Gleevec)FDA Link

Therapies and Procedures

1. Therapeutics
2. Drug Therapy (Chemotherapy)
3. Bloodletting
4. Stem Cell Transplantation
5. Contraindications