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Familial Mediterranean Fever (Periodic Disease)

A group of HEREDITARY AUTOINFLAMMATION DISEASES, characterized by recurrent fever, abdominal pain, headache, rash, PLEURISY; and ARTHRITIS. ORCHITIS; benign MENINGITIS; and AMYLOIDOSIS may also occur. Homozygous or compound heterozygous mutations in marenostrin gene encoding PYRIN result in autosomal recessive transmission; simple heterozygous, autosomal dominant form of the disease also exists with mutations in the same gene.
Also Known As:
Periodic Disease; Mediterranean Fever, Familial; Wolff Periodic Disease; Benign Paroxysmal Peritonitis; Familial Mediterranean Fever, Autosomal Dominant; Familial Mediterranean Fever, Autosomal Recessive; Familial Paroxysmal Polyserositis; Periodic Peritonitis; Polyserositis, Familial Paroxysmal; Polyserositis, Recurrent; Recurrent Polyserositis; Benign Paroxysmal Peritonitides; Disease, Periodic; Disease, Wolff Periodic; Disease, Wolff's Periodic; Diseases, Periodic; Familial Paroxysmal Polyserositides; Paroxysmal Peritonitides, Benign; Paroxysmal Peritonitis, Benign; Paroxysmal Polyserositides, Familial; Paroxysmal Polyserositis, Familial; Periodic Disease, Wolff; Periodic Disease, Wolffs; Periodic Diseases; Periodic Peritonitides; Peritonitides, Benign Paroxysmal; Peritonitides, Periodic; Peritonitis, Benign Paroxysmal; Peritonitis, Periodic; Polyserositides, Familial Paroxysmal; Polyserositides, Recurrent; Recurrent Polyserositides; Wolffs Periodic Disease; Periodic Disease, Wolff's; Wolff's Periodic Disease
Networked: 1604 relevant articles (101 outcomes, 159 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Amyloidosis
2. Gout
3. Pericarditis
4. Fever (Fevers)
5. Familial Mediterranean Fever (Periodic Disease)

Experts

1. Livneh, Avi: 42 articles (04/2022 - 04/2003)
2. Ozen, Seza: 37 articles (12/2022 - 05/2003)
3. Lidar, Merav: 21 articles (04/2022 - 12/2003)
4. Kastner, Daniel L: 20 articles (01/2022 - 01/2003)
5. Migita, Kiyoshi: 19 articles (01/2022 - 05/2013)
6. Ben-Zvi, Ilan: 18 articles (04/2022 - 04/2011)
7. Kawakami, Atsushi: 17 articles (07/2022 - 05/2013)
8. Tufan, Abdurrahman: 15 articles (12/2022 - 10/2006)
9. Koga, Tomohiro: 15 articles (07/2022 - 04/2016)
10. Ozdogan, Huri: 15 articles (01/2022 - 07/2003)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Familial Mediterranean Fever:
1. ColchicineFDA LinkGeneric
2. canakinumabFDA Link
3. Interleukin 1 Receptor Antagonist Protein (Anakinra)FDA Link
4. Interleukin-1 (Interleukin 1)IBA
5. AA amyloidosisIBA
6. Interferon-alpha (Interferon Alfa)IBA
7. rilonaceptFDA Link
8. tocilizumab (atlizumab)FDA Link
9. Infliximab (Remicade)FDA Link
10. Amyloid (Amyloid Fibrils)IBA

Therapies and Procedures

1. Therapeutics
2. Biological Therapy
3. Bone Marrow Transplantation (Transplantation, Bone Marrow)
4. Tonsillectomy
5. Thyroidectomy