A urea cycle enzyme that catalyzes the formation of orthophosphate and L-citrulline (CITRULLINE) from CARBAMOYL PHOSPHATE and L-ornithine (ORNITHINE). Deficiency of this enzyme may be transmitted as an X-linked trait. EC 2.1.3.3.
Also Known As:
Ornithine Transcarbamylase; Ornithine Carbamylphosphate Transferase; Carbamoyltransferase, Ornithine; Carbamylphosphate Transferase, Ornithine; Transcarbamylase, Ornithine; Transferase, Ornithine Carbamylphosphate; Carbamoyl-phosphate:L-ornithine carbamoyltransferase