A noninflammatory, progressive occlusion of the intracranial CAROTID ARTERIES and the formation of netlike collateral arteries arising from the CIRCLE OF WILLIS. Cerebral angiogram shows the puff-of-smoke (moyamoya) collaterals at the base of the brain. It is characterized by endothelial HYPERPLASIA and FIBROSIS with thickening of arterial walls. This disease primarily affects children but can also occur in adults.
Also Known As:
Moya-Moya Disease; Moyamoya Disease, Classic; Moyamoya Disease, Primary; Moyamoya Disease, Secondary; Moyamoya Syndrome; Classic Moyamoya Disease; Disease, Classic Moyamoya; Disease, Moya-Moya; Disease, Primary Moyamoya; Moya Moya Disease; Moyamoya Diseases, Primary; Primary Moyamoya Disease; Primary Moyamoya Diseases; Secondary Moyamoya Disease; Cerebrovascular Moyamoya Disease; Progressive Intracranial Occlusive Arteropathy (Moyamoya)