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Hyperlipoproteinemia Type III (Broad Beta Disease)

An autosomal recessively inherited disorder characterized by the accumulation of intermediate-density lipoprotein (IDL or broad-beta-lipoprotein). IDL has a CHOLESTEROL to TRIGLYCERIDES ratio greater than that of VERY-LOW-DENSITY LIPOPROTEINS. This disorder is due to mutation of APOLIPOPROTEINS E, a receptor-binding component of VLDL and CHYLOMICRONS, resulting in their reduced clearance and high plasma levels of both cholesterol and triglycerides.
Also Known As:
Broad Beta Disease; Familial Dysbetalipoproteinemia; Familial Hypercholesterolemia with Hyperlipemia; Hypercholesterolemia, Autosomal Recessive; Hyperlipoproteinemia, Broad-beta; Hyperlipoproteinemia, Type III; Autosomal Recessive Hypercholesterolemias; Broad-beta Hyperlipoproteinemia; Hyperlipoproteinemia, Broad beta; Hyperlipoproteinemias, Type III; Recessive Hypercholesterolemia, Autosomal; Type III Hyperlipoproteinemia; Type III Hyperlipoproteinemias; Autosomal Recessive Hypercholesterolemia; Dysbetalipoproteinemia; Dysbetalipoproteinemia, Familial
Networked: 539 relevant articles (25 outcomes, 43 trials/studies)

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Disease Context: Research Results

Related Diseases

1. Hyperlipoproteinemia Type III (Broad Beta Disease)
2. Hyperlipoproteinemia Type II (Familial Hypercholesterolemia)
3. Hyperlipidemias (Hyperlipidemia)
4. Cardiovascular Diseases (Cardiovascular Disease)
5. Dyslipidemias (Dyslipidemia)

Experts

1. Marais, A David: 10 articles (10/2022 - 01/2003)
2. Arca, Marcello: 8 articles (11/2020 - 11/2002)
3. Matsunaga, Akira: 7 articles (09/2015 - 02/2006)
4. Traub, Linton M: 7 articles (06/2014 - 12/2002)
5. Harada-Shiba, Mariko: 6 articles (06/2022 - 06/2003)
6. Bertolini, Stefano: 6 articles (11/2020 - 10/2006)
7. Saito, Takao: 6 articles (09/2015 - 02/2002)
8. Inazu, Akihiro: 6 articles (01/2015 - 10/2004)
9. Kobayashi, Junji: 6 articles (01/2015 - 10/2004)
10. Mabuchi, Hiroshi: 6 articles (01/2015 - 10/2004)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Hyperlipoproteinemia Type III:
1. Lipoproteins (Lipoprotein)IBA
2. Apolipoprotein E2IBA
3. Triglycerides (Triacylglycerol)IBA
4. LipidsIBA
5. Gemfibrozil (Lopid)FDA LinkGeneric
6. ClofibrateFDA Link
7. ApolipoproteinsIBA
8. LDL Receptors (LDL Receptor)IBA
9. LDL CholesterolIBA
10. Lovastatin (Mevacor)FDA LinkGeneric

Therapies and Procedures

1. Therapeutics
2. Combination Drug Therapy (Combination Chemotherapy)
3. Blood Component Removal (Apheresis)
4. Plasmapheresis
5. Fat-Restricted Diet (Diet, Fat Restricted)