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Hirschsprung Disease (Hirschsprung's Disease)

Congenital MEGACOLON resulting from the absence of ganglion cells (aganglionosis) in a distal segment of the LARGE INTESTINE. The aganglionic segment is permanently contracted thus causing dilatation proximal to it. In most cases, the aganglionic segment is within the RECTUM and SIGMOID COLON.
Also Known As:
Hirschsprung's Disease; Congenital Megacolon; Aganglionic Megacolon; Aganglionosis, Rectosigmoid Colon; Aganglionosis, Total Colonic; Congenital Intestinal Aganglionosis; Megacolon, Aganglionic; Rectosigmoid Aganglionosis; Total Colonic Aganglionosis; Aganglionosis, Rectosigmoid; Disease, Hirschsprung; Disease, Hirschsprung's; Hirschsprungs Disease; Rectosigmoid Colon Aganglionosis; Aganglionosis, Colonic; Colonic Aganglionosis; Megacolon, Congenital
Networked: 1458 relevant articles (33 outcomes, 147 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Ganglion Cysts (Ganglion)
2. Enterocolitis
3. Anorectal Malformations
4. Intestinal Pseudo-Obstruction (Intestinal Pseudoobstruction)
5. Megacolon

Experts

1. Puri, Prem: 25 articles (08/2020 - 10/2005)
2. Tang, Weibing: 22 articles (01/2022 - 08/2014)
3. Li, Hongxing: 21 articles (01/2022 - 08/2014)
4. Yamataka, Atsuyuki: 18 articles (05/2022 - 12/2002)
5. Xia, Yankai: 15 articles (01/2021 - 08/2014)
6. Coyle, David: 14 articles (08/2020 - 05/2015)
7. O'Donnell, Anne Marie: 14 articles (08/2020 - 05/2015)
8. Xie, Hua: 13 articles (01/2020 - 05/2015)
9. Du, Chunxia: 12 articles (01/2022 - 01/2016)
10. Miyahara, Katsumi: 11 articles (05/2022 - 05/2007)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Hirschsprung Disease:
1. AcetylcholinesteraseIBA
2. Calbindin 2IBA
3. Eosine Yellowish-(YS) (Eosin)IBA
4. Hematoxylin (Haematoxylon)IBA
5. Glial Cell Line-Derived Neurotrophic Factor (GDNF)IBA
6. EnzymesIBA
7. Adrenergic Agents (Adrenergic Drugs)IBA
8. Neurotransmitter Agents (Neurotransmitter)IBA
9. Adenosine Triphosphate (ATP)IBA
10. TeaIBA

Therapies and Procedures

1. Colostomy
2. Enema (Enemas)
3. Operative Surgical Procedures
4. Therapeutics
5. Colectomy