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Glycogen Storage Disease Type VI (Glycogenosis Type VI)

A hepatic GLYCOGEN STORAGE DISEASE in which there is an apparent deficiency of hepatic phosphorylase (GLYCOGEN PHOSPHORYLASE, LIVER FORM) activity.
Also Known As:
Glycogenosis Type VI; Hers' Disease; Glycogenosis VI; Hepatic Glycogen Phosphorylase Deficiency; Liver Phosphorylase Deficiency Syndrome; Disease, Hers; Disease, Hers'; Her Disease; Type VI, Glycogenosis; Glycogenosis 6; Hers Disease
Networked: 586 relevant articles (57 outcomes, 12 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Disease Progression
2. Pain (Aches)
3. Neoplasm Metastasis (Metastasis)
4. Hemorrhage
5. Multiple Myeloma

Experts

1. Hannibal, Luciana: 2 articles (03/2021 - 01/2021)
2. Spiekerkoetter, Ute: 2 articles (03/2021 - 01/2021)
3. Prohászka, Zoltán: 2 articles (01/2021 - 11/2014)
4. Pagnoux, Christian: 2 articles (10/2020 - 10/2011)
5. Bisht, Niharika: 2 articles (07/2019 - 10/2018)
6. Husain, Azhar: 2 articles (07/2019 - 10/2018)
7. Purkayastha, Abhishek: 2 articles (07/2019 - 10/2018)
8. Singh, Sankalp: 2 articles (07/2019 - 10/2018)
9. Kitagawa, Yuko: 2 articles (11/2015 - 08/2009)
10. Castells, Mariana: 2 articles (09/2012 - 01/2012)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Glycogen Storage Disease Type VI:
1. SteroidsIBA
2. Adrenal Cortex Hormones (Corticosteroids)IBA
3. Methotrexate (Mexate)FDA LinkGeneric
4. Cyclophosphamide (Cytoxan)FDA LinkGeneric
5. Rituximab (Mabthera)FDA Link
6. Prednisolone (Predate)FDA LinkGeneric
7. Intravenous Immunoglobulins (IVIG)FDA Link
8. AntibodiesIBA
9. Etoposide (VP 16)FDA LinkGeneric
10. Infliximab (Remicade)FDA Link

Therapies and Procedures

1. Therapeutics
2. Drug Therapy (Chemotherapy)
3. Plasma Exchange
4. Stem Cell Transplantation
5. Immunotherapy