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Focal Segmental Glomerulosclerosis (Glomerulosclerosis, Focal)

A clinicopathological syndrome or diagnostic term for a type of glomerular injury that has multiple causes, primary or secondary. Clinical features include PROTEINURIA, reduced GLOMERULAR FILTRATION RATE, and EDEMA. Kidney biopsy initially indicates focal segmental glomerular consolidation (hyalinosis) or scarring which can progress to globally sclerotic glomeruli leading to eventual KIDNEY FAILURE.
Also Known As:
Glomerulosclerosis, Focal; Glomerulosclerosis, Focal Segmental; Hyalinosis, Segmental; Segmental Glomerular Hyalinosis; Focal Glomerulosclerosis; Focal Sclerosing Glomerulonephritides; Focal Sclerosing Glomerulonephritis; Glomerular Hyalinosis, Segmental; Glomerulonephritides, Focal Sclerosing; Sclerosing Glomerulonephritides, Focal; Sclerosing Glomerulonephritis, Focal; Segmental Glomerulosclerosis, Focal; Segmental Hyalinosis; Glomerulonephritis, Focal Sclerosing; Hyalinosis, Segmental Glomerular
Networked: 2121 relevant articles (130 outcomes, 160 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Nephrotic Syndrome (Syndrome, Nephrotic)
2. Proteinuria
3. Lipoid Nephrosis (Glomerulonephritis, Minimal Change)
4. Membranous Glomerulonephritis (Membranous Nephropathy)
5. IGA Glomerulonephritis (IGA Nephropathy)

Experts

1. Trachtman, Howard: 31 articles (05/2022 - 10/2004)
2. Kopp, Jeffrey B: 31 articles (02/2022 - 02/2006)
3. Reiser, Jochen: 26 articles (01/2022 - 07/2005)
4. Ghiggeri, Gian Marco: 24 articles (10/2021 - 01/2001)
5. Wei, Changli: 19 articles (01/2022 - 07/2005)
6. Gipson, Debbie S: 19 articles (01/2021 - 01/2007)
7. Wetzels, Jack F M: 17 articles (01/2022 - 07/2002)
8. Kretzler, Matthias: 16 articles (02/2022 - 07/2003)
9. Pollak, Martin R: 15 articles (01/2022 - 07/2005)
10. Candiano, Giovanni: 15 articles (10/2021 - 01/2001)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Focal Segmental Glomerulosclerosis:
1. SteroidsIBA
2. Cyclosporine (Ciclosporin)FDA LinkGeneric
3. Rituximab (Mabthera)FDA Link
4. Adrenocorticotropic Hormone (ACTH)FDA Link
5. Adrenal Cortex Hormones (Corticosteroids)IBA
6. oxidized low density lipoproteinIBA
7. Prednisone (Sone)FDA LinkGeneric
8. Tacrolimus (Prograf)FDA LinkGeneric
9. LDL Lipoproteins (beta Lipoproteins)IBA
10. Cyclophosphamide (Cytoxan)FDA LinkGeneric

Therapies and Procedures

1. Therapeutics
2. Plasmapheresis
3. Kidney Transplantation
4. Transplantation
5. Blood Component Removal (Apheresis)