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Galactosylceramidase

An enzyme that hydrolyzes galactose from ceramide monohexosides. Deficiency of this enzyme may cause globoid cell leukodystrophy (LEUKODYSTROPHY, GLOBOID CELL). EC 3.2.1.46.
Also Known As:
Galactosylceramide Galactosidase; Galactosylceramide beta-Galactosidase; Galactosylcerebroside beta-Galactosidase; Galactosidase, Galactosylceramide; beta-Galactosidase, Galactosylceramide; beta-Galactosidase, Galactosylcerebroside; Galactocerebrosidase; D-Galactosyl-N-acylsphingosine galactohydrolase
Networked: 370 relevant articles (4 outcomes, 5 trials/studies)

Relationship Network

Bio-Agent Context: Research Results

Experts

1. Wenger, David A: 22 articles (08/2021 - 04/2004)
2. Sands, Mark S: 16 articles (01/2021 - 09/2005)
3. Bongarzone, Ernesto R: 15 articles (01/2021 - 12/2007)
4. Rafi, Mohammad A: 12 articles (08/2021 - 05/2005)
5. Luzi, Paola: 11 articles (08/2021 - 05/2005)
6. Martino, Sabata: 11 articles (01/2021 - 03/2009)
7. Escolar, Maria L: 10 articles (01/2021 - 09/2015)
8. Gritti, Angela: 10 articles (01/2021 - 03/2009)
9. Orsini, Joseph J: 9 articles (05/2021 - 09/2015)
10. Costantino-Ceccarini, Elvira: 9 articles (04/2017 - 05/2009)

Related Diseases

1. Globoid Cell Leukodystrophy (Krabbe Disease)
2. Central Nervous System Diseases (CNS Diseases)
3. Demyelinating Diseases (Demyelinating Disease)
4. Neurodegenerative Diseases (Neurodegenerative Disease)
5. Lysosomal Storage Diseases (Lysosomal Storage Disease)

Related Drugs and Biologics

1. Enzymes
2. Psychosine (Galactosylsphingosine)
3. DNA (Deoxyribonucleic Acid)
4. Galactosylceramides (Galactocerebrosides)
5. beta-Galactosidase (Lactaid)
6. Proteins (Proteins, Gene)
7. Hydrolases
8. galactocerebroside
9. Saposins
10. Complementary DNA (cDNA)

Related Therapies and Procedures

1. Bone Marrow Transplantation (Transplantation, Bone Marrow)
2. Cell Transplantation
3. Therapeutics
4. Enzyme Replacement Therapy
5. Hematopoietic Stem Cell Transplantation