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Polyostotic Fibrous Dysplasia (McCune Albright Syndrome)

FIBROUS DYSPLASIA OF BONE affecting several bones. When melanotic pigmentation (CAFE-AU-LAIT SPOTS) and multiple endocrine hyperfunction are additionally associated it is referred to as Albright syndrome.
Also Known As:
McCune Albright Syndrome; Albright Syndrome; Syndrome, Albright's; Syndrome, McCune-Albright; Albright's Syndrome; Fibrous Dysplasia, Polyostotic; Albright's Disease; Albright's Disease of Bone; Albright's Syndrome with Precocious Puberty; Albright-Mccune-Sternberg Syndrome; Albright-Sternberg Syndrome; Fibrous Dysplasia with Pigmentary Skin Changes and Precocious Puberty; Dysplasia, Polyostotic Fibrous; Dysplasias, Polyostotic Fibrous; Fibrous Dysplasias, Polyostotic; Polyostotic Fibrous Dysplasias; Syndrome, Albright; McCune-Albright Syndrome
Networked: 407 relevant articles (20 outcomes, 16 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Precocious Puberty
2. Cushing Syndrome
3. Neoplasms (Cancer)
4. Pituitary Neoplasms (Pituitary Adenoma)
5. Gynecomastia

Experts

1. Collins, Michael T: 16 articles (12/2021 - 09/2003)
2. Boyce, Alison M: 9 articles (01/2022 - 02/2016)
3. Stratakis, Constantine A: 9 articles (01/2021 - 07/2004)
4. Eugster, Erica A: 7 articles (01/2016 - 07/2003)
5. Lala, Roberto: 6 articles (01/2018 - 01/2002)
6. Riminucci, Mara: 5 articles (12/2020 - 09/2003)
7. Matarazzo, Patrizia: 5 articles (01/2018 - 05/2006)
8. Zacharin, Margaret: 5 articles (01/2018 - 03/2002)
9. Sultan, Charles: 5 articles (12/2015 - 12/2006)
10. Cherman, Natasha: 5 articles (06/2008 - 09/2003)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Polyostotic Fibrous Dysplasia:
1. Testolactone (Teslac)FDA Link
2. Gonadotropin-Releasing Hormone (GnRH)FDA Link
3. Aromatase InhibitorsIBA
4. Alendronate (Alendronate Sodium)FDA LinkGeneric
5. Letrozole (Femara)FDA LinkGeneric
6. MetyraponeFDA Link
7. Pamidronate (Aredia)FDA LinkGeneric
8. TamoxifenFDA LinkGeneric
9. Estrogen Receptor AntagonistsIBA
10. Fulvestrant (Faslodex)FDA Link

Therapies and Procedures

1. Therapeutics
2. Ovariectomy (Oophorectomy)
3. Radiotherapy
4. Adrenalectomy
5. Aftercare (After-Treatment)