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Myoclonic Epilepsies (Myoclonic Encephalopathy)

A clinically diverse group of epilepsy syndromes characterized either by myoclonic seizures or by myoclonus in association with other seizure types. Myoclonic epilepsy syndromes are divided into three subtypes based on etiology: familial, cryptogenic, and symptomatic.
Also Known As:
Myoclonic Encephalopathy; Epilepsy, Myoclonus; Epilepsy, Myoclonic; Myoclonus Epilepsy; Myoclonic Epilepsy; Epilepsies, Myoclonic; Benign Infantile Myoclonic Epilepsy; Cryptogenic Myoclonic Epilepsy; Doose Syndrome; Dravet Syndrome; Early Childhood Epilepsy, Myoclonic; Early Childhood, Myoclonic Epilepsy; Encephalopathy, Myoclonic; Epilepsy, Early Childhood, Myoclonic; Epilepsy, Myoclonic, Early Childhood; Epilepsy, Myoclonic, Infantile; Epilepsy, Myoclonic, Infantile, Benign; Epilepsy, Myoclonic, Infantile, Severe; Infantile Severe Myoclonic Epilepsy; Myoclonic Astatic Epilepsy; Myoclonic Epilepsy, Benign Infantile; Myoclonic Epilepsy, Early Childhood; Myoclonic Epilepsy, Infantile; Myoclonic Epilepsy, Infantile, Benign; Myoclonic Epilepsy, Infantile, Severe; Myoclonic Epilepsy, Severe Infantile; Myoclonic Epilepsy, Severe, Of Infancy; Myoclonic Seizure Disorder; Severe Infantile Myoclonic Epilepsy; Severe Myoclonic Epilepsy Of Infancy; Severe Myoclonic Epilepsy, Infantile; Astatic Epilepsies, Myoclonic; Astatic Epilepsy, Myoclonic; Cryptogenic Myoclonic Epilepsies; Dravet Syndromes; Encephalopathies, Myoclonic; Epilepsies, Cryptogenic Myoclonic; Epilepsies, Idiopathic Myoclonic; Epilepsies, Infantile Myoclonic; Epilepsies, Myoclonic Absence; Epilepsies, Myoclonic Astatic; Epilepsies, Symptomatic Myoclonic; Epilepsy, Cryptogenic Myoclonic; Epilepsy, Idiopathic Myoclonic; Epilepsy, Infantile Myoclonic; Epilepsy, Myoclonic Absence; Epilepsy, Myoclonic Astatic; Epilepsy, Symptomatic Myoclonic; Idiopathic Myoclonic Epilepsies; Infantile Myoclonic Epilepsies; Infantile Myoclonic Epilepsy; Myoclonic Absence Epilepsies; Myoclonic Astatic Epilepsies; Myoclonic Encephalopathies; Myoclonic Epilepsies, Cryptogenic; Myoclonic Epilepsies, Idiopathic; Myoclonic Epilepsies, Infantile; Myoclonic Epilepsies, Symptomatic; Myoclonic Epilepsy, Cryptogenic; Myoclonic Epilepsy, Idiopathic; Myoclonic Epilepsy, Symptomatic; Myoclonic Seizure Disorders; Myoclonus Epilepsies; Seizure Disorder, Myoclonic; Seizure Disorders, Myoclonic; Symptomatic Myoclonic Epilepsies; Idiopathic Myoclonic Epilepsy; Myoclonic Absence Epilepsy; Symptomatic Myoclonic Epilepsy
Networked: 1199 relevant articles (100 outcomes, 142 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Lennox Gastaut Syndrome
2. Seizures (Absence Seizure)
3. Epilepsy (Aura)
4. Myoclonic Epilepsies (Myoclonic Encephalopathy)
5. Infantile Spasms (West Syndrome)

Experts

1. Scheffer, Ingrid E: 30 articles (11/2022 - 02/2002)
2. Nabbout, Rima: 24 articles (01/2022 - 07/2004)
3. Catterall, William A: 22 articles (01/2021 - 09/2006)
4. Striano, Pasquale: 21 articles (01/2022 - 03/2006)
5. Hirose, Shinichi: 20 articles (05/2022 - 09/2002)
6. Yamakawa, Kazuhiro: 20 articles (11/2021 - 05/2002)
7. Ceulemans, Berten: 17 articles (01/2022 - 07/2004)
8. Kearney, Jennifer A: 17 articles (01/2022 - 09/2005)
9. Lagae, Lieven: 17 articles (12/2021 - 07/2004)
10. Chiron, Catherine: 17 articles (01/2020 - 07/2005)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Myoclonic Epilepsies:
1. CannabidiolIBA
2. FenfluramineIBA
3. stiripentolIBA
4. Valproic Acid (Depakote)FDA LinkGeneric
5. Anticonvulsants (Antiepileptic Drugs)IBA
6. Clobazam (HR 376)IBA
7. Topiramate (Topamax)FDA LinkGeneric
8. perampanelIBA
9. Levetiracetam (Keppra)FDA LinkGeneric
10. BromidesIBA

Therapies and Procedures

1. Therapeutics
2. Ketogenic Diet
3. Induced Hyperthermia (Thermotherapy)
4. High-Protein Low-Carbohydrate Diet (Atkins Diet)
5. Drug Therapy (Chemotherapy)