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Hemophilia B (Haemophilia B)

A deficiency of blood coagulation factor IX inherited as an X-linked disorder. (Also known as Christmas Disease, after the first patient studied in detail, not the holy day.) Historical and clinical features resemble those in classic hemophilia (HEMOPHILIA A), but patients present with fewer symptoms. Severity of bleeding is usually similar in members of a single family. Many patients are asymptomatic until the hemostatic system is stressed by surgery or trauma. Treatment is similar to that for hemophilia A. (From Cecil Textbook of Medicine, 19th ed, p1008)
Also Known As:
Haemophilia B; Christmas Disease; Factor IX Deficiency; Deficiency, Factor IX; F9 Deficiency; Hemophilia B Leyden; Hemophilia B(M); Plasma Thromboplastin Component Deficiency; Bs, Hemophilia; Deficiencies, F9; Deficiencies, Factor IX; Deficiency, F9; Disease, Christmas; F9 Deficiencies; Factor IX Deficiencies; Haemophilia Bs; Hemophilia Bs; Hemophilia Bs (M)
Networked: 1910 relevant articles (107 outcomes, 247 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Hemorrhage
2. Hemophilia A (Haemophilia)
3. Body Weight (Weight, Body)
4. Anaphylaxis (Anaphylactic Shock)
5. Thrombosis (Thrombus)

Experts

1. High, Katherine A: 39 articles (01/2020 - 04/2002)
2. Herzog, Roland W: 37 articles (10/2021 - 04/2002)
3. Nichols, Timothy C: 25 articles (01/2022 - 04/2002)
4. Arruda, Valder R: 20 articles (02/2021 - 04/2002)
5. Mingozzi, Federico: 19 articles (01/2022 - 01/2004)
6. Santagostino, Elena: 16 articles (05/2020 - 01/2011)
7. Pierce, Glenn F: 15 articles (12/2017 - 01/2006)
8. Monahan, Paul E: 14 articles (11/2021 - 09/2004)
9. Castaman, Giancarlo: 12 articles (01/2022 - 01/2008)
10. Santagostino, E: 12 articles (10/2020 - 10/2004)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Hemophilia B:
1. Factor IX (Coagulation Factor IX)FDA LinkGeneric
2. Proteins (Proteins, Gene)FDA Link
3. prothrombin complex concentrates (PPSB)IBA
4. nonacog beta pegolIBA
5. Factor VIII (Coagulation Factor VIII)IBA
6. factor IX Fc fusion proteinIBA
7. Blood Coagulation Factors (Coagulation Factor)IBA
8. Hemostatics (Antihemorrhagics)IBA
9. AlbuminsIBA
10. AntigensIBA

Therapies and Procedures

1. Therapeutics
2. Intramuscular Injections
3. Cell- and Tissue-Based Therapy (Cell Therapy)
4. Intravenous Administration
5. Intravenous Infusions