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Biliary Atresia

Progressive destruction or the absence of all or part of the extrahepatic BILE DUCTS, resulting in the complete obstruction of BILE flow. Usually, biliary atresia is found in infants and accounts for one third of the neonatal cholestatic JAUNDICE.
Also Known As:
Biliary Atresia, Extrahepatic; Biliary Atresia, Intrahepatic; Extrahepatic Biliary Atresia; Familial Extrahepatic Biliary Atresia; Idiopathic Extrahepatic Biliary Atresia; Intrahepatic Biliary Atresia; Atresia, Extrahepatic Biliary; Atresia, Intrahepatic Biliary; Atresia, Biliary
Networked: 2290 relevant articles (91 outcomes, 223 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Jaundice (Icterus)
2. Cholangitis
3. End Stage Liver Disease
4. Neonatal hemochromatosis
5. Liver Diseases (Liver Disease)

Experts

1. Bezerra, Jorge A: 39 articles (10/2022 - 11/2002)
2. Poovorawan, Yong: 37 articles (01/2022 - 01/2002)
3. Sokol, Ronald J: 33 articles (01/2022 - 11/2002)
4. Zheng, Shan: 31 articles (08/2022 - 06/2007)
5. Chongsrisawat, Voranush: 30 articles (03/2022 - 01/2002)
6. Chen, Chao-Long: 28 articles (10/2021 - 02/2004)
7. Vejchapipat, Paisarn: 27 articles (01/2022 - 07/2004)
8. Honsawek, Sittisak: 25 articles (01/2022 - 02/2005)
9. Mack, Cara L: 24 articles (10/2022 - 07/2004)
10. Dong, Rui: 24 articles (08/2022 - 10/2012)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Biliary Atresia:
1. SteroidsIBA
2. Bile Acids and Salts (Bile Acids)IBA
3. BilirubinIBA
4. VaccinesIBA
5. Octreotide (Sandostatin)FDA LinkGeneric
6. Rifampin (Rifampicin)FDA LinkGeneric
7. Biomarkers (Surrogate Marker)IBA
8. Proteins (Proteins, Gene)FDA Link
9. Adrenal Cortex Hormones (Corticosteroids)IBA
10. Ursodeoxycholic Acid (Urso)FDA LinkGeneric

Therapies and Procedures

1. Liver Transplantation
2. Hepatic Portoenterostomy
3. Therapeutics
4. Laparotomy
5. Transplantation