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Renal Tubular Acidosis (Distal Renal Tubular Acidosis)

A group of genetic disorders of the KIDNEY TUBULES characterized by the accumulation of metabolically produced acids with elevated plasma chloride, hyperchloremic metabolic ACIDOSIS. Defective renal acidification of URINE (proximal tubules) or low renal acid excretion (distal tubules) can lead to complications such as HYPOKALEMIA, hypercalcinuria with NEPHROLITHIASIS and NEPHROCALCINOSIS, and RICKETS.
Also Known As:
Distal Renal Tubular Acidosis; Renal Tubular Acidosis, Distal, Autosomal Dominant; Acidosis, Renal Tubular; Acidosis, Renal Tubular, Type I; Acidosis, Renal Tubular, Type II; Autosomal Dominant Distal Renal Tubular Acidosis; Classic Distal Renal Tubular Acidosis; Proximal Renal Tubular Acidosis; RTA, Classic Type; RTA, Distal Type, Autosomal Dominant; RTA, Gradient Type; RTA, Proximal Type; Renal Tubular Acidosis 1; Renal Tubular Acidosis I; Renal Tubular Acidosis II; Renal Tubular Acidosis, Proximal; Renal Tubular Acidosis, Proximal, with Ocular Abnormalities; Classic Type RTA; Classic Type RTAs; Gradient Type RTA; Gradient Type RTAs; Proximal Type RTA; Proximal Type RTAs; RTAs, Classic Type; RTAs, Gradient Type; RTAs, Proximal Type; Renal Tubular Acidosis, Type I; Renal Tubular Acidosis, Type II; Type I Renal Tubular Acidosis; Type II Renal Tubular Acidosis
Networked: 1252 relevant articles (27 outcomes, 63 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Fanconi Syndrome (Syndrome, Fanconi)
2. Hypokalemia
3. Glycosuria
4. Acidosis
5. Osteomalacia

Experts

1. Wagner, Carsten A: 25 articles (06/2020 - 03/2002)
2. Cordat, Emmanuelle: 18 articles (01/2020 - 12/2002)
3. Alper, Seth L: 12 articles (01/2020 - 01/2002)
4. Reithmeier, Reinhart A F: 12 articles (01/2018 - 12/2002)
5. Sawasdee, Nunghathai: 11 articles (01/2017 - 07/2002)
6. Yenchitsomanus, Pa-Thai: 11 articles (01/2017 - 01/2003)
7. Mohebbi, Nilufar: 10 articles (06/2020 - 01/2006)
8. Yenchitsomanus, Pa-thai: 10 articles (07/2014 - 07/2002)
9. Eladari, Dominique: 9 articles (03/2020 - 12/2010)
10. Trepiccione, Francesco: 8 articles (12/2021 - 11/2016)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Renal Tubular Acidosis:
1. AlkaliesIBA
2. Furosemide (Lasix)FDA LinkGeneric
3. Phosphates (Orthophosphate)IBA
4. FludrocortisoneIBA
5. dirhodium tetraacetate (DRTA)IBA
6. Potassium CitrateFDA LinkGeneric
7. Uric Acid (Urate)IBA
8. PotassiumIBA
9. Ammonium Chloride (Sal Ammoniac)FDA Link
10. potassium bicarbonateIBA

Therapies and Procedures

1. Therapeutics
2. Kidney Transplantation
3. Aftercare (After-Treatment)
4. Hormone Replacement Therapy (Therapy, Hormone Replacement)
5. Orthopedic Procedures