monomelic Amyotrophy

01/01/2010 - "Thus, our study supports the notion that Hirayama disease is a benign self-limited disorder with juvenile preponderance and asymmetric muscular atrophy of the distal portion of the upper limb. "
05/01/2008 - "The purpose of this study was to review the clinical manifestations of 40 patients who fulfilled the clinical criteria for Hirayama disease (juvenile muscular atrophy of distal upper extremities), identified in our neuromuscular clinic between February 1995 and December 2005. "
04/01/2015 - "Hirayama disease is a rare children's muscular atrophy that affects young Asian males, with muscular atrophy usually in one of the upper limbs that progresses slowly and later stabilises. "
11/01/2013 - "Its other synonyms are juvenile muscular atrophy of the distal upper extremity (JMADUE) or monomelic amyotrophy (MMA). "
07/01/2012 - "Hirayama disease is a juvenile muscular atrophy of the distal upper extremities and affects mainly young males. "

02/01/1998 - "In nonflexion studies, we find that asymmetric cord atrophy, especially at the lower cervical cord, though subtle, is highly suggestive of Hirayama disease. "
08/01/2015 - "Clinico-radiologic profile of the patient leads toward the diagnosis of Hirayama disease which was considered as borderline because of asymmetrical cord atrophy which is a not a routine imaging feature of the entity. "
04/01/2014 - "Hirayama disease is characterized by asymmetrical focal weakness and atrophy of the distal upper limbs with onset in the teens and early 20s. "
11/15/2013 - "Hirayama disease (HD) is a rare motor disorder mainly affecting young men, characterized by atrophy and weakness of forearm and hand muscles corresponding to a C7-T1 myotome distribution. "
10/01/2013 - "We describe an atypical case of Hirayama disease (HD) presenting as unilateral triceps atrophy. "

03/01/2012 - "Results of our study challenge the hypothesis that Hirayama disease is a type of cervical myelopathy."
11/01/2014 - "Dynamic myelopathy in Hirayama disease."
11/01/2014 - "The clinical improvements achieved by the authors' method support evidence that a tight dural canal in flexion largely contributes to segmental myelopathy in patients with Hirayama disease."
06/01/2014 - "Hirayama disease is an uncommon cervical myelopathy associated with neck flexion. "
02/01/2014 - "Hirayama disease, or juvenile amyotrophy of distal upper extremity, is a benign, self-limiting cervical myelopathy consisting of selective unilateral weakness of the hand and forearm. "

08/01/2011 - "The purpose of this study was to compare the pattern of hand muscle involvement in Hirayama disease (HD) and amyotrophic lateral sclerosis (ALS). "
01/01/2014 - "Electrophysiological differences between Hirayama disease, amyotrophic lateral sclerosis and cervical spondylotic amyotrophy."
10/15/2014 - "Lower motor neuron dysfunction restricted to the C7-T1 myotomes in the absence of neuropathy, upper motor neuron signs, sphincter disturbances or abnormality on conventional MR imaging is suggestive of either Hirayama disease (HD), or the initial manifestation of a progressive motor neuron disease such as amyotrophic lateral sclerosis (ALS). "
01/01/2014 - "Hirayama disease (HD), amyotrophic lateral sclerosis (ALS) or cervical spondylotic amyotrophy (CSA) may result in atrophy of intrinsic hand and forearm muscles. "

07/01/2014 - "Hirayama disease (HD) is rare, but benign anterior horn cell disease, predominantly affecting young men. "
10/01/2013 - "Monomelic amyotrophy (MMA) is a benign, self-limiting lower motor neuron disease. "
04/01/2012 - "Hirayama disease (HD) is benign focal amyotrophy of the distal upper limbs, often misdiagnosed as motor neuron disease. "
07/01/2011 - "Monomelic amyotrophy (MMA) is a benign motor neuron disease characterized by neurogenic amyotrophy, which usually affects one of the upper or lower extremities. "
05/01/2008 - "Our results support the belief that Hirayama disease is a self-limited, focal lower motor neuron disease involving the lower cervical segments. "