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Saccharopinuria

Also Known As:
Alpha-aminoadipic semialdehyde synthase deficiency; Saccharopine dehydrogenase deficiency
Networked: 10 relevant articles (0 outcomes, 1 trials/studies)

Bio-Agent Context: Research Results

Experts

1. Funai, Asuka: 1 article (05/2021)
2. Kawata, Akihiro: 1 article (05/2021)
3. Kuhara, Tomiko: 1 article (05/2021)
4. Miyamoto, Kazuhito: 1 article (05/2021)
5. Nagao, Masayoshi: 1 article (05/2021)
6. Nishigori, Ryusei: 1 article (05/2021)
7. Norioka, Ryohei: 1 article (05/2021)
8. Ohura, Toshihiro: 1 article (05/2021)
9. Takahashi, Kazushi: 1 article (05/2021)
10. Takai, Yasuyuki: 1 article (05/2021)

Related Diseases

1. Hyperlysinemias (Hyperlysinemia)
2. Cognitive Dysfunction
3. Mitochondrial Diseases (Mitochondrial Disease)
4. Hyperammonemia
5. Gait Ataxia

Related Drugs and Biologics

1. Lysine (L-Lysine)
2. saccharopine
3. Saccharopine Dehydrogenases (Saccharopine Dehydrogenase (NAD+, L-Glutamate Forming))
4. Ornithine
5. HHH syndrome