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Alpha-ketoglutarate dehydrogenase deficiency

Also Known As:
2 alpha ketoglutarate dehydrogenase deficiency; 2-Ketoglutarate Dehydrogenase Deficiency; Oxoglutaric Aciduria; Oxoglutaricaciduria
Networked: 4 relevant articles (0 outcomes, 0 trials/studies)

Disease Context: Research Results

Related Diseases

1. Cognitive Dysfunction
2. Multiple Acyl Coenzyme A Dehydrogenase Deficiency
3. Central Nervous System Cavernous Hemangioma
4. Multiple Carboxylase Deficiency (Deficiency, Multiple Carboxylase)
5. Mucopolysaccharidoses

Experts

1. Barrio, Raquel: 1 article (12/2017)
2. Cabrejas Núñez, María José: 1 article (12/2017)
3. Castaño, Luis: 1 article (12/2017)
4. López, Gilberto Pérez: 1 article (12/2017)
5. Quispe, Beatriz Villafuerte: 1 article (12/2017)
6. Bonnefont, Jean-Paul: 1 article (03/2005)
7. Chretien, Dominique: 1 article (03/2005)
8. Dumoulin, Renée: 1 article (03/2005)
9. Kadhom, Noman: 1 article (03/2005)
10. Masmoudi, Sahben: 1 article (03/2005)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Alpha-ketoglutarate dehydrogenase deficiency:
1. Dihydrolipoamide Dehydrogenase (Lipoamide Dehydrogenase)IBA
2. Insulin-Like Growth Factor Binding Protein 3IBA
3. Succinate Dehydrogenase (Fumarate Reductase)IBA
4. Aconitate Hydratase (Aconitase)IBA
5. Fumaric aciduriaIBA
6. 2-Methylacetoacetyl CoA thiolase deficiencyIBA