Idiopathic pulmonary hypertension

03/01/2006 - "This may be important in the future if new specific therapies for primary pulmonary hypertension are shown to be beneficial in secondary pulmonary hypertension. "
01/01/2009 - "It has been shown recently that similar pharmacotheraeutic approaches as they are used in patients with pulmonary arterial hypertension are effective in some cases of other forms of chronic pulmonary hypertension. "
08/11/2007 - "There have been tremendous progresses in research and improvement in therapeutic options for pulmonary arterial hypertension (PAH) and other types of pulmonary hypertension (PH) over the last 15 years. "
03/01/2006 - "However, although several new selective therapies are effective in idiopathic pulmonary arterial hypertension, their role in secondary pulmonary hypertension remains unclear."
09/01/2006 - "The efficacy of PDE5 inhibition in the treatment of pulmonary arterial hypertension has led to the investigation of its potential utility in the treatment of HF patients with secondary pulmonary hypertension. "

03/01/1985 - "We conclude that there are some Echo-Phonocardiographic signs which are very useful in the diagnosis and measurement of pulmonary arterial hypertension in children with congenital heart disease."
09/20/2013 - "Efficacy of exercise training in pulmonary arterial hypertension associated with congenital heart disease."
12/01/2014 - "24 patients with congenital heart disease-associated pulmonary arterial hypertension, including 4 receiving heart surgery and 20 with surgical contraindications, were enrolled in this study. "
11/01/2013 - "The present study aims to determine the relationship between the cardiac catheterization findings and PW Doppler and Doppler tissue imaging (DTI) in patients who have pulmonary arterial hypertension patients due to congenital heart disease with intracardiac shunts. "
11/01/2013 - "The aim of this study is to determine the relationship between the cardiac catheterization findings and pulsed-wave (PW) Doppler and Doppler tissue imaging (DTI) in pulmonary arterial hypertension patients with congenital heart disease with intracardiac shunts. "

05/01/2010 - "Despite improved understanding of the pathobiology of pulmonary arterial hypertension (PAH), it remains a severe and progressive disease, usually culminating in right heart failure, significant morbidity and early mortality. "
07/01/2007 - "They have been shown to be effective in the management of primary pulmonary hypertension, but disappointing in heart failure. "
11/01/2013 - "Restoring and enhancing the physiological protective role of ETB1-signaling with concomitant blockade of ETB2 could possibly improve the efficacy of current therapies in the setting of pulmonary arterial hypertension and post-ischemic chronic heart failure. "
04/01/2015 - "[Short-term efficacy of atrial septostomy in the treatment of idiopathic pulmonary arterial hypertension patients complicating with right heart failure]."
11/01/2009 - "We reported two cases of severe idiopathic pulmonary hypertension in children with right heart failure refractory to medical treatment who benefited of Potts shunt."

01/01/2013 - "This is a rare case of rapidly progressive pulmonary arterial hypertension associated with systemic sclerosis that can be markedly improved with early diagnosis and treatment."
04/01/2009 - "Pulmonary arterial hypertension in systemic sclerosis: can we predict responders for successful therapy?"
04/01/2012 - "Pulmonary arterial hypertension therapy may be safe and effective in patients with systemic sclerosis and borderline pulmonary artery pressure."
06/01/2007 - "Pulmonary arterial hypertension (PAH) has poor prognosis in systemic sclerosis (SSc), and at present the "gold standard" for diagnosis and follow-up of PAH in SSc is right heart catheterization (RHC) but it would be very useful to have a noninvasive way to follow these patients. "
10/01/2013 - "Survival in systemic sclerosis with pulmonary arterial hypertension has not improved in the modern era."

11/01/2015 - "Studies suggest that patients with connective tissue disease-associated pulmonary arterial hypertension (CTD-PAH) have a poorer treatment response to therapies for PAH compared with patients with idiopathic PAH (IPAH), but individual randomized controlled trials (RCTs) have been underpowered to examine differences within these subgroups. "
01/01/2013 - "Pulmonary arterial hypertension associated with connective tissue disease: meta-analysis of clinical trials."
11/01/2008 - "To study the epidemiology, clinical characteristics and prognosis of children with pulmonary arterial hypertension (PAH) secondary to connective tissue disease (CTD). "
07/01/2005 - "The prevalence of undiagnosed pulmonary arterial hypertension in subjects with connective tissue disease at the secondary health care level of community-based rheumatologists (the UNCOVER study)."
11/01/2015 - "Screening and Early Detection of Pulmonary Arterial Hypertension in Connective Tissue Diseases. "