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Islet cell tumor syndrome

Hereditary PHEOCHROMOCYTOMA that originates in ISLET CELLS. Affected individuals have systemic symptoms that may include cerebral hemorrhage, episodic hypertension, sweating, TACHYCARDIA; HYPERTENSIVE RETINOPATHY; CAFÉ-AU-LAIT SPOTS; and excess NOREPINEPHRINE in urine. OMIM: 171420
Also Known As:
Bilateral pheochromocytoma and islet cell adenoma of the pancreas; Chromaffinoma; Familial islet cell tumors; Familial pheochromocytoma
Networked: 50 relevant articles (0 outcomes, 4 trials/studies)

Disease Context: Research Results

Related Diseases

1. Pheochromocytoma
2. Hypertension (High Blood Pressure)
3. Paraganglioma (Paragangliomas)
4. Neoplasms (Cancer)
5. Multiple Endocrine Neoplasia Type 2a (MEN 2)

Experts

1. Kaelin, William G: 3 articles (01/2019 - 08/2005)
2. Brauckhoff, Michael: 3 articles (05/2008 - 12/2003)
3. Dralle, Henning: 3 articles (05/2008 - 12/2003)
4. Gimm, Oliver: 3 articles (05/2008 - 12/2003)
5. Schlisio, Susanne: 2 articles (01/2019 - 08/2005)
6. Cascon, Alberto: 2 articles (12/2017 - 02/2008)
7. Eisenhofer, G: 2 articles (10/2009 - 02/2001)
8. Pacak, K: 2 articles (10/2009 - 02/2001)
9. Brauckhoff, Katrin: 2 articles (05/2008 - 12/2003)
10. Thanh, Phuong Nguyen: 2 articles (05/2008 - 12/2003)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Islet cell tumor syndrome:
1. CatecholaminesIBA
2. Vanilmandelic Acid (Vanillylmandelic Acid)IBA
3. Estradiol (Delestrogen)FDA LinkGeneric
4. CreatinineIBA
5. Succinate Dehydrogenase (Fumarate Reductase)IBA
6. EnzymesIBA
7. Retinaldehyde (Retinal)IBA
8. Norepinephrine (Noradrenaline)FDA LinkGeneric
9. Hydrocortisone (Cortisol)FDA LinkGeneric
10. Epinephrine (Adrenaline)FDA LinkGeneric

Therapies and Procedures

1. Adrenalectomy
2. Therapeutics
3. Splenectomy