2-methyl-3-hydroxybutyryl-coenzyme A dehydrogenase (2-methyl-3-hydroxybutyryl-CoA dehydrogenase)
reaction:(2S,3S)-3-hydroxy-2-methylbutanoyl-CoA + NAD+ = 2-methylacetoacetyl-CoA + NADH; deficiency is associated with progressive infantile neurodegeneration
Also Known As:
2-methyl-3-hydroxybutyryl-CoA dehydrogenase; (2S,3S)-3-hydroxy-2-methylbutanoyl-CoA + NAD+ - oxidoreductase; 2-MHB-CoA dehydrogenase
Networked: 5
relevant articles (0 outcomes,
0 trials/studies)
Bio-Agent Context: Research Results
Experts
1. | Ofman, Rob:
2 articles
(09/2005 - 04/2004)
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2. | Wanders, Ronald J A:
2 articles
(09/2005 - 04/2004)
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3. | Bernard, Geneviève:
1 article
(12/2019)
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4. | Boucher, Renée-Myriam:
1 article
(12/2019)
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5. | Buhas, Daniela:
1 article
(12/2019)
|
6. | Cyr, Denis:
1 article
(12/2019)
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7. | Gravel, Serge:
1 article
(12/2019)
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8. | Lace, Baiba:
1 article
(12/2019)
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9. | Lévesque, Sébastien:
1 article
(12/2019)
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10. | Maranda, Bruno:
1 article
(12/2019)
|
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